Solid Pseudopapillary Neoplasm of the Pancreas: Radiological, Clinical, Histopathological and Prognostic Features of 5 Patients

Yıl 2023, Cilt: 5 Sayı: 3, 233 - 238, 01.11.2023

Nuray Çolapkulu Nesrin Gündüz Humeyra Gunel Mehmet Sait Özsoy Orhan Alimoğlu

https://doi.org/10.38175/phnx.1300358

Öz

Solid pseudopapillary neoplasms of the pancreas are rare lesions, classified as borderline malignant tumors. They predominantly affect younger females and have more favorable outcomes compared to other pancreatic tumors. While patients may present with non-specific symptoms, the use of imaging modalities has led to an increase in incidental cases. These neoplasms are typically diagnosed using radiological imaging methods due to their characteristic features. Unlike pancreatic adenocarcinomas, surgical treatment results in lower morbidity rates and disease-free survival rates above ninety percent. This study aims to report the clinical, histopathological, and prognostic features of five cases of solid pseudopapillary neoplasms of the pancreas and review the current literature.

Anahtar Kelimeler

Pseudopapillary tumor, pancreas, incidental tumors

Pankreasın Solid Psödopapiller Neoplazmı: 5 Hastanın Radyolojik, Klinik, Histopatolojik ve Prognostik Özellikleri

Öz

Pankreasın solid psödopapiller neoplazmaları nadir lezyonlardır ve borderline malign tümor olarak sınıflandırılır. Daha çok genç yaştaki kadınlarda görülürler ve pankreasın diğer tümörlerine kıyasla daha iyi prognoza sahiptirler. Hastalar spesifik olmayan semptomlarla başvurabilir, ancak insidental vakaların sayısı son yıllarda görüntüleme yöntemlerinin yoğun kullanımının bir sonucu olarak artmıştır. Tümörlerin karakteristik özellikleri ile çoğunlukla radyolojik görüntüleme yöntemleri ile teşhis edilirler. Pankreas adenokarsinomlarından farklı olarak cerrahi ile morbidite oranları daha düşüktür ve hastalıksız sağ kalım oranları yüzde doksanın üzerindedir. Bu çalışmada beş pankreas solid psödopapiller neoplazi olgusunun klinik, histopatolojik ve prognostik özelliklerini sunmayı ve literatürün güncel durumunu gözden geçirmeyi amaçladık.

Anahtar Kelimeler

Psödopapiller tümör, Pankreas

Kaynakça

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