With Nursing Perspective: Creutzfeldt Jacob Disease

Öz

Creutzfeldt-Jakob disease (CJH); is a prion disease that occurs with symptoms of cognitive and mental state deterioration, cerebellar ataxia, myoclonic movements and vision loss. It is important to distinguish it from other diseases as it progresses rapidly and causes death. From laboratory studies, EEG is initially non-specific, and in the middle and advanced stages of the disease, periodic sharp wave discharges typically occur every 0.5-2 seconds. Its annual incidence has been reported as one in a million. The application of patients with different clinical features makes it difficult to recognize the disease. The prognosis of the disease is fast and complex, affecting the patient and family negatively in term of physically, socioeconomically and psychologically. In this disease group, where multi-faceted care needs can occur, nurses can provide a patient-centered and evidence-based care to increase the quality of life patient and their family. Another issue that concerns nurses who are in constant contact with the patient and provide care is infection control. In this article, care needs that can occur in CJH patients and nursing approaches are examined.

Anahtar Kelimeler

• Creutzfeldt-Jakob Disease
• Patient-Centered Nursing
• Continuum of Care

Hemşirelik Bakış Açısı İle: Creutzfeldt Jacob Hastalığı

Öz

Creutzfeldt-Jakob hastalığı (CJH); bilişsel ve ruhsal durumda bozulma, serebellar ataksi, miyoklonik hareketler ve görme kaybı bulguları ile ortaya çıkan bir prion hastalığıdır. Hızla ilerleyerek ölüme sebep olması nedeni ile diğer hastalıklardan ayırt edilmesi önemlidir. Laboratuvar incelemelerinden EEG’de başlangıçta özgül olmayan bulgular, hastalığın orta ve ileri dönemlerinde ise tipik olarak 0.5-2 saniyede bir oluşan periyodik keskin dalga deşarjları görülür. Yıllık görülme sıklığı milyonda bir olarak bildirilmiştir. Hastaların farklı klinik özelliklerle başvurması hastalığın tanınmasını güçleştirmektedir. Hastalığın prognozunun hızlı ve karmaşık olması hasta ve ailesini fiziki, sosyoekonomik ve psikolojik yönden olumsuz etkilemektedir. Çok yönlü bakım gereksinimlerinin oluşabildiği bu hastalık grubunda hemşireler, hasta merkezli ve kanıta dayalı bir bakım sunarak hasta ve ailesinin yaşam kalitesinde artış sağlayabilirler. Hastayla sürekli temas halinde bulunan ve bakım veren hemşireleri ilgilendiren bir diğer konu da enfeksiyon kontrolüdür. Bu makalede, CJH hastalarında oluşabilecek bakım gereksinimleri ve hemşirelik yaklaşımları incelenmiştir.

Anahtar Kelimeler

• Creutzfeldt jacob hastalığı
• hemşirelik
• bakım

Kaynakça

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