Anesthesia Management Of A Patient With Neurofibromatosis

Yıl 2016, Cilt: 8 Sayı: 2, 75 - 78, 24.07.2016

Hakan Bayır

Öz

Neurofibromatosis is an autosomal dominant and multisistemic disorder characterized by the formation of tumours. There are two types of Neurofibromatosis (NF); NF1 and NF2. NF 1 is more commonly seen and neurofibromas can be found in multiple systems. In this case report, anesthetic management of neurofibromatosis was reviewed in a patient with neurofibroma extending from L1 vertebrae to the sacrum in the lumbar region.

Anahtar Kelimeler

Neurofibromatosis, general anesthesia, neurofibroma

Nörofîbromatozisli Hastada Anestezi Yönetimi

Öz

Nörofibromatozis, otozomal dominant geçişli, tümöral oluşumla karakterize multi-sistemik bir hastalıktır. NF1 ve NF2 olarak iki tipi vardır. NF 1 daha sık görülüp, nö-rofibromlar birden fazla sistemde bulunabilir. Genel anestezi ve rejyonel anestezi uygulaması bu hastalarda özellik taşır. Bu olgu sunumunda, bel bölgesinde L1 ver-tebradan sakruma kadar uzanan büyüklükteki nörofibromla beraber tüm vücudunda yaygın nörofibromları olan olguda nörofibromatozisde anestezi yönetimi gözden geçirildi.

Dr. Hakan BAYIR
Dr. Recai DAĞLI
Dr. Nazan KOCAOGLU
Dr. İsa YILDIZ

Anahtar Kelimeler

Nörofibromatozis, genel anestezi, nörofibrom

Kaynakça

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