Amniotic Band Syndrome: A Case Report

Abstract

Amniotic band syndrome causes a wide spectrum of fetal anomalies secondary to the early rupture of the amnion. Its prevalence ranges between one in 1200 and 15000 live-born and reaches one in 56 in stillbirths. Although a wide range of malformations can occur in this syndrome, extremities are frequently involved. The prognosis depends on the severity of the abnormalities and the involvement of internal organs. Herein a case of amniotic band syndrome which caused medical evacuation for intauterin defect in a 24 years old primigravid woman was submitted. There was no history of maternal illness, drug use or trauma. In the fetal autopsy, the fetus was in the 14-15 th gestational week, and several extremity anomalies were found. Amniotic Band Syndrome should be kept in mind in the differential diagnosis of fetal anomalies, especially with extremity involvement. Key words: Amniotic Band Syndrome; Intauterin Defect; Fetal Anomaly.

Keywords

• Amniotic Band Syndrome; Intauterin Defect; Fetal Anomaly.

Amniyotik Band Senromu: Olgu Sunumu

Öz

Amniotik band sendromu, amnion zarının erken rüptürüne bağlı gelişen, geniş bir fetal anomali spektrumuna sebep olur. ABS prevelansı 1/1200 ile 1/15000 arasında değişebilmekte, spontan abortuslarda 1/56'ya kadar çıkabilmektedir. Bu sendromda geniş bir dizi malformasyon ortaya çıkabilmesine karşılık ekstremiteler sıklıkla tutulmuştur. Prognoz anomalilerin şiddetine ve iç organ tutulumuna bağlıdır. Burada 24 yaşında, ilk gebeliği olan kadında, intraterin defekt nedeni ile tıbbi tahliyeye neden olan amniotik band sendromu olgusu sunulmuştur. Annede herhangi bir hastalık, ilaç kullanımı veya travma öyküsü yoktu. Fetal otopside 14-15. gestasyonel haftada olan fetusda çeşitli ekstremite anomalileri tespit edildi. ABS özellikle ekstemite anomalileriyle birlikte giden fetal anomalilerin ayırıcı tanısında akılda tutulmalıdır. Anahtar kelimeler: Amniotik Band Sendromu; İntrauterin Defekt; Fetal Anomali.

Anahtar Kelimeler

• Amniotik Band Sendromu; İntrauterin Defekt; Fetal Anomali.

Kaynakça

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