Critical Care Management of Amyotrophic Lateral Sclerosis Cases

Abstract

Amyotrophic lateral sclerosis (ALS) is a progressive, neurodegenerative disease caused by the degeneration of motor neurons, including medulla spinalis, cerebellum and motor cortex of central nervous system that control voluntary muscle movement. The disease usually does not affect cognitive abilities, but makes muscle weakness, difficulty in swallowing and chewing especially breathing. Here in, we report the critical care management of three ALS case with pneumonia and severe respiratory distress. Key words: Amyotrophic Lateral Sclerosis, Motor Neuron Disease, Critical Care, Pneumonia

Keywords

• Amyotrophic Lateral Sclerosis, Motor Neuron Disease, Critical Care, Pneumonia

Amyotrofik Lateral Skleroz Olgularında Yoğun Bakım Tedavisi

Öz

Amyotrofik lateral skleroz (ALS) medülla spinalis, beyin sapı ve beynin motor korteksindeki motor nöronların ilerleyici dejeneratif bir hastalığıdır. Bilinç bozukluğu yapmadan yaygın kas güçsüzlüğü, yutma güçlüğü ve özellikle solunum güçlüğü yaratan bir hastalıktır. Bu yazıda ağır solunum yetmezliği ve pnömoniyle yoğun bakımda takip ve tedavi edilen üç ALS tanısı almış olgunun takip ve tedavisi sunulmuştur. Anahtar kelimeler: Amyotrofik Lateral Skleroz, Motor Nöron Hastalığı, Yoğun Bakım, Pnömoni

Anahtar Kelimeler

• Amyotrofik Lateral Skleroz, Motor Nöron Hastalığı, Yoğun Bakım, Pnömoni

Kaynakça

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