Behçet Disease and Parkinsonism

Öz

Behcet's syndome is a multi systemic disease of unknown etiology characterized by oral and genital ulcers, and uveitis. Ophtalmological, dermatological, gastrointestinal, and neurological involvement can be seen. Central nervous system involvement is rarely an initial presenting manifestation of Behçet's disease. In Neurobehcet syndrome brainstem syndrome and meningoencefalitis are mostly described. Basal ganglia involvement is rare in Neurobehcet. Parkinsonism with Neurobehcet syndrome is rare in literature. Therefore we report a case of neurobehcet disease and parkinsonism Key words: Behçet disease, Parkinsonism, Movement disorders.

Anahtar Kelimeler

• Behçet disease, Parkinsonism, Movement disorders.

Behçet Hastalığı ve Parkinsonizm

Öz

Behçet hastalığı etyolojisi bilinmeyen, oral ve genital ülserler ve uveit ile kendini gösteren multi-sistemik bir hastalıktır. Oftalmik, deri, gastrointestinal ve nörolojik tutulum görülebilir. Santral sinir sistemi tutulumu nadiren Behçet hastalığının başlangıç bulgusu olarak görülür. Nörobehçet hastalığında sıklıkla meningoensefalit ve beyin sapı sendromu tanımlanmıştır. Bazal gangliyon tutulumu nadirdir. Literatürde Behçet hastalığına bağlı parkinsonizm az sayıda yayınlanmıştır. Bu nedenle nörobehçet hastalığı ve parkinsonizm tablosu olan vakamızı sunuma değer bulduk. Anahtar kelimeler: Behçet hastalığı, Parkinsonizm, Hareket bozuklukları.

Anahtar Kelimeler

• Behçet hastalığı, Parkinsonizm, Hareket bozuklukları.

Kaynakça

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