Cystic neuroblastoma in a newborn: A case report

Yıl 2008, Cilt: 15 Sayı: 1, 39 - 41, 01.02.2008

Sema Uğuralp Ahmet Sığırcı Neşe Karadağ

Öz

An abdominal cystic mass with a 2.5x1.8 cm diameter was diagnosed in a 28 week- gestation female fetus using antenatal ultrasonography (US). Postnatal US confirmed a cystic mass in the right adrenal region. The abdominal computed tomography revealed a hypodense, thick walled cyst which pushed the right kidney to the lower side. Intraoperatively, the mass appeared to be within the right adrenal gland, and a right adrenalectomy was performed. Histology confirmed a poorly differentiated neuroblastoma. Cystic neuroblastoma (CNB) should be considered in the differential diagnosis of suprarenal cystic masses. It can be suggested that any cystic adrenal mass with characteristic US sign (thick wall) in a neonate must be removed since there is a probability of malignancy. Key words: Neuroblastoma, Neonate, Cystic, Prenatal

Anahtar Kelimeler

Neuroblastoma, Neonate, Cystic, Prenatal

Bir Yenidoğanda Kistik Nöroblastoma: Olgu Sunumu

Öz

Yirmisekiz haftalık kız fetüste antenatal ultrasonografide (US) 2.5x1.8 cm çaplı abdominal kistik kitle saptandı. Postnatal yapılan US de kistik kitlenin sağ adrenal bölgede olduğu görüldü. Abdominal kompüterize tomografide hipodens, sağ böbreği aşağı iten kalın duvarlı kist mevcuttu. Ameliyatta kitlenin sağ adrenal glandda olduğu görüldü ve sağ adrenalektomi yapıldı. Histolojik olarak kitle az diferensiye nöroblastoma olarak değerlendirildi. Suprarenal kistik kitlelerin ayırıcı tanısında kistik nöroblastoma (CNB) düşünülmelidir. US de karakteristik olarak kalın duvarlı kistik kitlesi olan bir yenidoğanda kitlenin malign olabilme ihtimaline karşı çıkarılmasını öneriyoruz. Anahtar kelimeler: Nöroblastoma, Yenidoğan, Kist, Prenatal

Anahtar Kelimeler

Nöroblastoma, Yenidoğan, Kist, Prenatal

Kaynakça

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• Department of Pediatric Surgery, Turgut Ozal Medical Center, Inonu University, Faculty of Medicine, 44069 Malatya, Turkey. Phone :[phone] Fax : [phone]
• E-mail : [e-mail]