Melkersson-Rosenthal syndrome: a case report on a child

Yıl 2009, Cilt: 19 Sayı: 2, 99 - 102, 12.03.2009

Hayrullah Alp Haluk Yavuz Esma Alp

Öz

Melkersson-Rosenthal syndrome MRS includes the triad of oro-facial edema, facial nerve palsy and furrowed tongue. The exact etiology is unknown. However, genetic and acquired factors have been implicated. It is rare in children. In this study, we report a ten year old boy who was diagnosed with MRS with recurrent facial nerve paralysis and facial edema.

Anahtar Kelimeler

Childhood, facial edema, facial nerve palsy, Melkersson-Rosenthal syndrome

Melkersson-Rosenthal sendromu: Bir çocuk olgunun sunumu

Öz

Melkersson-Rosenthal sendromu MRS ; yüzde ödem, yedinci sinir felci ve yarık dil ile kendini gösteren bir sendromdur. Kesin nedeni belli değildir. Kalıtımsal veya sonradan olan etkenlerin yol açabileceği düşü- nülmektedir. Çocuklarda nadir olarak görülür. Bu yazı- da 10 yaşında, tekrarlayan yüz felci ve yüzde ödem ile MRS tanısı konan bir erkek olgu sunuldu

Anahtar Kelimeler

Çocukluk çağı, yüz ödemi, yedinci sinir felci, Melkersson-Rosenthal sendromu

Kaynakça

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