Down Sendromlu Yenidoğanda Asemptomatik Sağ Bochdalek Hernisi

Abstract

Konjenital diyafragma hernisi, diyafragmada defektler sonucu gelişen kalıtsal anomalilerdir. Diyafragmadaki konjenital defektten dolayı abdominal yapılar torakal kaviteye herniyason yapar. Akciğer grafisinde bağırsak anslarının toraksta görülmesi büyük oranda tanı koydurur. Diyafragma hernileri özefageal hiatustan (hiatal), paraözefageal, retrosternal (Morgagni) veya posterolateral (Bochdalek) bölgelerden gelişebilir. Bu olgu sunumunda Down sendromlu yenidoğan bir bebeğin sağ Bochdalek hernisi tanı süreci, cerrahi işlemi ve literatür karşılaştırması anlatılmıştır.

Keywords

• Bochdalek hernisi
• diafragma
• laparaskopi
• yenidoğan

A Down Syndrome-Newborn with Asymptomatic Right Bochdalek Hernia

Abstract

ABSTRACT:

Congenital diaphragmatic hernia is hereditary anomalies resulting from defects in the diaphragm. Abdominal structures herniate into the thoracic cavity due to congenital defect in the diaphragm. For accurate diagnosis, the presence of bowel loops in the thorax is decisive on the chest radiograph. Diaphragmatic hernias may develop from esophageal hiatus (hiatal), paraesophageal, retrosternal (Morgagni) or posterolateral (Bochdalek) regions. In this case report, the diagnosis and surgical procedure of a Down syndrome-newborn baby with right Bochdalek hernia was discussed by comparison of the literature.

Keywords

• Bochdalek hernia
• diaphragma
• newborn
• laparoscopy

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