Down Sendromlu Yenidoğanda Asemptomatik Sağ Bochdalek Hernisi

Yıl 2020, , 178 - 183, 31.08.2020

Olena Erkun , Tetyana Syrotenko Aybars Özkan , İbrahim Caner , Öner Özdemir , Ayşegül Pala

https://doi.org/10.34084/bshr.742765

Öz

Konjenital diyafragma hernisi, diyafragmada defektler sonucu gelişen kalıtsal anomalilerdir. Diyafragmadaki konjenital defektten dolayı abdominal yapılar torakal kaviteye herniyason yapar. Akciğer grafisinde bağırsak anslarının toraksta görülmesi büyük oranda tanı koydurur. Diyafragma hernileri özefageal hiatustan (hiatal), paraözefageal, retrosternal (Morgagni) veya posterolateral (Bochdalek) bölgelerden gelişebilir. Bu olgu sunumunda Down sendromlu yenidoğan bir bebeğin sağ Bochdalek hernisi tanı süreci, cerrahi işlemi ve literatür karşılaştırması anlatılmıştır.

Anahtar Kelimeler

Bochdalek hernisi, diafragma, laparaskopi, yenidoğan

A Down Syndrome-Newborn with Asymptomatic Right Bochdalek Hernia

Öz

ABSTRACT:

Congenital diaphragmatic hernia is hereditary
anomalies resulting from defects in the diaphragm. Abdominal structures
herniate into the thoracic cavity due to congenital defect in the diaphragm.
For accurate diagnosis, the presence of bowel loops in the thorax is decisive
on the chest radiograph. Diaphragmatic hernias may develop from esophageal
hiatus (hiatal), paraesophageal, retrosternal (Morgagni) or posterolateral
(Bochdalek) regions. In this case report, the diagnosis and surgical procedure
of a Down syndrome-newborn baby with right Bochdalek hernia was discussed by
comparison of the literature.

Anahtar Kelimeler

Bochdalek hernia, diaphragma, newborn, laparoscopy

Kaynakça

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