Anaesthetic management of a patient with hereditary angioedema
Abstract
Hereditary angioedema is a rare autosomal dominant disorder caused by reduced activity of the C1 esterase inhibitor. Patients with hereditary angioedema are clinically characterized by recurrent episodes of swelling of the extremities, face, trunk, airways and abdominal organs. Attacks may occur either spontaneously or following trauma, stress, surgery, infections and hormonal fluctuations. The most common cause of death is asphyxia related to laryngeal edema. Giving C1 esterase inhibitor is the most effective method of treatment. Also fresh frozen plasma, androgen steroids, quinine pathway inhibitors, antifibrinolytics and bradykinin receptor antagonists can be used as treatment. In this paper, the anesthetic management of a patient with hereditary angioedema undergoing inguinal hernia repair surgery is reported.
Key words: Hereditary angioedema; C1 esterase inhibitor; Inguinal hernia
Keywords
References
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Details
Primary Language
Turkish
Subjects
-
Journal Section
-
Authors
Nergis Ataol
This is me
Murat Öksüz
This is me
Feride Korkmaz
This is me
Alaattin Öztürk
This is me
Publication Date
January 8, 2016
Submission Date
January 8, 2016
Acceptance Date
-
Published in Issue
Year 2015 Volume: 42 Number: 4