Anaesthetic management of a patient with hereditary angioedema
Öz
Hereditary angioedema is a rare autosomal dominant disorder caused by reduced activity of the C1 esterase inhibitor. Patients with hereditary angioedema are clinically characterized by recurrent episodes of swelling of the extremities, face, trunk, airways and abdominal organs. Attacks may occur either spontaneously or following trauma, stress, surgery, infections and hormonal fluctuations. The most common cause of death is asphyxia related to laryngeal edema. Giving C1 esterase inhibitor is the most effective method of treatment. Also fresh frozen plasma, androgen steroids, quinine pathway inhibitors, antifibrinolytics and bradykinin receptor antagonists can be used as treatment. In this paper, the anesthetic management of a patient with hereditary angioedema undergoing inguinal hernia repair surgery is reported.
Key words: Hereditary angioedema; C1 esterase inhibitor; Inguinal hernia
Anahtar Kelimeler
Kaynakça
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Ayrıntılar
Birincil Dil
Türkçe
Konular
-
Bölüm
-
Yazarlar
Nergis Ataol
Bu kişi benim
Murat Öksüz
Bu kişi benim
Feride Korkmaz
Bu kişi benim
Alaattin Öztürk
Bu kişi benim
Yayımlanma Tarihi
8 Ocak 2016
Gönderilme Tarihi
8 Ocak 2016
Kabul Tarihi
-
Yayımlandığı Sayı
Yıl 2015 Cilt: 42 Sayı: 4