RHABDOMYOSARCOMA IN A NEWBORN: CASE REPORT

Year 2021, Volume: 18 Issue: 4, 1099 - 1102, 31.12.2021

Aslı Genç Mustafa Şenol Akın Derya Özyörük Sevim Ünal

https://doi.org/10.38136/jgon.943740

Abstract

Although rhabdomyosarcoma is the most common soft tissue sarcoma in childhood, it is a very rare tumor in the neonatal period. It constitutes %5-8 of all malignant solid tumors in childhood. It is the third most common extracranial solid tumor of childhood and the most common soft tissue sarcoma after neuroblastoma and Wilms' tumor. Only %1-2 of all rhabdomyosarcomas occur in the neonatal period. It usually manifests as a growing mass anywhere on the body. The most common locations are the head-neck and genito-urinary system, close to the visceral organs such as the retroperitoneum, pelvis and abdomen, and the extremities. Here, we aimed to contribute to the literature by presenting a newborn born with a vaginal mass and diagnosed with botroid variant rhabdomyosarcoma.

Keywords

Newborn, rhabdomyosarcoma, congenital mass

BİR YENİDOĞANDA RABDOMYOSARKOM: OLGU SUNUMU

Abstract

Rabdomyosarkom çocukluk yaş grubunda en sık görülen yumuşak doku sarkomu olmakla birlikte, yenidoğan döneminde oldukça nadir rastlanan bir tümördür. Çocukluk çağındaki tüm malign solid tümörlerin %5-8'ini oluşturur. Nöroblastom ve Wilms tümöründen sonra çocukluk çağının üçüncü en yaygın ekstrakraniyal solid tümörü ve en yaygın yumuşak doku sarkomudur. Tüm rabdomyosarkomların ancak %1-2 kadarı yenidoğan döneminde görülür. Genellikle vücudun herhangi bir yerinde büyüyen bir kitle olarak bulgu verir. En sık yerleşim bölgeleri baş-boyun ve genito-üriner sistem olmak üzere retroperiton, pelvis ve batın gibi visseral organların komşuluğu ve ekstremitelerdir. Burada vajinal kitle ile doğan ve botroid varyant rabdomyosarkom tanısı alan bir yenidoğan sunularak literatüre katkıda bulunulmak istenmiştir.

Keywords

Yenidoğan, rabdomyosarkom, konjenital kitle

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