Pulmoner arteriyel hipertansiyon: tanı ve tedavisi

Önder Öztürk; Ünal Şahin

doi:10.17343/sdutfd.36555

Pulmoner arteriyel hipertansiyon: tanı ve tedavisi

Abstract

Süleyman Demirel Üniversitesi TIP FAKÜLTESİ DERGİSİ: 2009 Mart; 16 (1) Pulmoner arteriyel hipertansiyon: tanı ve tedavisi Önder Öztürk, Ünal Şahin Özet Pulmoner arteriyel hipertansiyon (PAH), altta yatan, sebebi bilinmeyen nadir bir hastalıktır. Pulmoner arteriyel hipertansiyon bulguları belirgin olmadığından sessiz seyreder. Ancak eforla artan dispne şikayeti olan olgularda şüphe edildiğinde ve nedeni bilinen PH olgularında tanı konulabilmektedir. PH şüphe edilen olgularda, iki boyutlu Doppler ekokardiyografi en yararlı tanı yöntemlerinden biridir. PH varlığında ise oksijenizasyon, akciğer fonksiyon testleri, yüksek rezolüsyonlu bilgisayarlı tomografi, ventilasyon-perfüzyon sintigrafisi ve kardiyak kateterizasyon gibi ileri tetkiklerin yapılması gerekir. Standart veya kombine tedavilerle egzersiz kapasitesinde, yaşam kalitesinde, hemodinamide ve yaşam süresinde iyileşme saptanır. Yeni tedavi yöntemleri ve ajanlarla PAH tedavisinde yüz güldürücü sonuçlar elde edilmektedir. Akciğer transplantasyonu, tıbbi tedaviye cevap vermeyen pulmoner arteriyel hipertansiyonu olan seçilmiş hastalarda bir umut olarak durmaktadır. Anahtar kelimeler: pulmoner arteriyel hipertansiyon, semptomlar, tanı, tedavi. Abstract Pulmonary arterial hypertension: diagnosis and treatment Pulmonary arterial hypertension (PAH) is a rare disease of unknown etiology. Signs and symptoms of pulmonary arterial hypertension are often subtle and nonspecific. The diagnosis should be suspected in patients with increasing dyspnea on exertion and a known cause of pulmonary hypertension. Two-dimensional echocardiography with Doppler flow studies is the most useful imaging modality in patients with suspected pulmonary hypertension. If pulmonary hypertension is present, further evaluation may include assessment of oxygenation, pulmonary function testing, high-resolution computed tomography of the chest, ventilation-perfusion lung scanning and cardiac catheterization. Treatment with standart or combination therapy improve exercise capacity, quality of life, hemodynamics and long-term survival in patients with PAH. New agents are also under examination with affirmative results. Lung transplantation remains an option for selected patients with pulmonary arterial hypertension that does not respond to medical management. Key words: pulmonary arterial hypertension, symptoms, diagnosis, treatment.

Keywords

pulmoner arteriyel hipertansiyon, semptomlar, taný, tedavi

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Details

Primary Language

English

Subjects

-

Journal Section

-

Authors

Önder Öztürk This is me

Ünal Şahin This is me

Publication Date

March 30, 2009

Submission Date

June 1, 2009

Acceptance Date

-

Published in Issue

Year 2009 Volume: 16 Number: 1

DOI

https://doi.org/10.17343/sdutfd.36555

IZ

https://izlik.org/JA62PX79DG

Cite

RIS / Bibtex

APA

Öztürk, Ö., & Şahin, Ü. (2009). Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Medical Journal of Süleyman Demirel University, 16(1), 39-47. https://doi.org/10.17343/sdutfd.36555

AMA

1.Öztürk Ö, Şahin Ü. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Med J SDU. 2009;16(1):39-47. doi:10.17343/sdutfd.36555

Chicago

Öztürk, Önder, and Ünal Şahin. 2009. “Pulmoner Arteriyel Hipertansiyon: Tanı Ve Tedavisi”. Medical Journal of Süleyman Demirel University 16 (1): 39-47. https://doi.org/10.17343/sdutfd.36555.

EndNote

Öztürk Ö, Şahin Ü (March 1, 2009) Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Medical Journal of Süleyman Demirel University 16 1 39–47.

IEEE

[1]Ö. Öztürk and Ü. Şahin, “Pulmoner arteriyel hipertansiyon: tanı ve tedavisi”, Med J SDU, vol. 16, no. 1, pp. 39–47, Mar. 2009, doi: 10.17343/sdutfd.36555.

ISNAD

Öztürk, Önder - Şahin, Ünal. “Pulmoner Arteriyel Hipertansiyon: Tanı Ve Tedavisi”. Medical Journal of Süleyman Demirel University 16/1 (March 1, 2009): 39-47. https://doi.org/10.17343/sdutfd.36555.

JAMA

1.Öztürk Ö, Şahin Ü. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Med J SDU. 2009;16:39–47.

MLA

Öztürk, Önder, and Ünal Şahin. “Pulmoner Arteriyel Hipertansiyon: Tanı Ve Tedavisi”. Medical Journal of Süleyman Demirel University, vol. 16, no. 1, Mar. 2009, pp. 39-47, doi:10.17343/sdutfd.36555.

Vancouver

1.Önder Öztürk, Ünal Şahin. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Med J SDU. 2009 Mar. 1;16(1):39-47. doi:10.17343/sdutfd.36555