Pulmoner arteriyel hipertansiyon: tanı ve tedavisi

Önder Öztürk; Ünal Şahin

doi:10.17343/sdutfd.36555

Pulmoner arteriyel hipertansiyon: tanı ve tedavisi

Öz

Süleyman Demirel Üniversitesi TIP FAKÜLTESİ DERGİSİ: 2009 Mart; 16 (1) Pulmoner arteriyel hipertansiyon: tanı ve tedavisi Önder Öztürk, Ünal Şahin Özet Pulmoner arteriyel hipertansiyon (PAH), altta yatan, sebebi bilinmeyen nadir bir hastalıktır. Pulmoner arteriyel hipertansiyon bulguları belirgin olmadığından sessiz seyreder. Ancak eforla artan dispne şikayeti olan olgularda şüphe edildiğinde ve nedeni bilinen PH olgularında tanı konulabilmektedir. PH şüphe edilen olgularda, iki boyutlu Doppler ekokardiyografi en yararlı tanı yöntemlerinden biridir. PH varlığında ise oksijenizasyon, akciğer fonksiyon testleri, yüksek rezolüsyonlu bilgisayarlı tomografi, ventilasyon-perfüzyon sintigrafisi ve kardiyak kateterizasyon gibi ileri tetkiklerin yapılması gerekir. Standart veya kombine tedavilerle egzersiz kapasitesinde, yaşam kalitesinde, hemodinamide ve yaşam süresinde iyileşme saptanır. Yeni tedavi yöntemleri ve ajanlarla PAH tedavisinde yüz güldürücü sonuçlar elde edilmektedir. Akciğer transplantasyonu, tıbbi tedaviye cevap vermeyen pulmoner arteriyel hipertansiyonu olan seçilmiş hastalarda bir umut olarak durmaktadır. Anahtar kelimeler: pulmoner arteriyel hipertansiyon, semptomlar, tanı, tedavi. Abstract Pulmonary arterial hypertension: diagnosis and treatment Pulmonary arterial hypertension (PAH) is a rare disease of unknown etiology. Signs and symptoms of pulmonary arterial hypertension are often subtle and nonspecific. The diagnosis should be suspected in patients with increasing dyspnea on exertion and a known cause of pulmonary hypertension. Two-dimensional echocardiography with Doppler flow studies is the most useful imaging modality in patients with suspected pulmonary hypertension. If pulmonary hypertension is present, further evaluation may include assessment of oxygenation, pulmonary function testing, high-resolution computed tomography of the chest, ventilation-perfusion lung scanning and cardiac catheterization. Treatment with standart or combination therapy improve exercise capacity, quality of life, hemodynamics and long-term survival in patients with PAH. New agents are also under examination with affirmative results. Lung transplantation remains an option for selected patients with pulmonary arterial hypertension that does not respond to medical management. Key words: pulmonary arterial hypertension, symptoms, diagnosis, treatment.

Anahtar Kelimeler

pulmoner arteriyel hipertansiyon, semptomlar, taný, tedavi

Kaynakça

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Ayrıntılar

Birincil Dil

İngilizce

Konular

-

Bölüm

-

Yazarlar

Önder Öztürk Bu kişi benim

Ünal Şahin Bu kişi benim

Yayımlanma Tarihi

30 Mart 2009

Gönderilme Tarihi

1 Haziran 2009

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2009 Cilt: 16 Sayı: 1

DOI

https://doi.org/10.17343/sdutfd.36555

IZ

https://izlik.org/JA62PX79DG

Kaynak Göster

RIS / Bibtex

APA

Öztürk, Ö., & Şahin, Ü. (2009). Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Medical Journal of Süleyman Demirel University, 16(1), 39-47. https://doi.org/10.17343/sdutfd.36555

AMA

1.Öztürk Ö, Şahin Ü. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. SDÜ Tıp Fak Derg. 2009;16(1):39-47. doi:10.17343/sdutfd.36555

Chicago

Öztürk, Önder, ve Ünal Şahin. 2009. “Pulmoner arteriyel hipertansiyon: tanı ve tedavisi”. Medical Journal of Süleyman Demirel University 16 (1): 39-47. https://doi.org/10.17343/sdutfd.36555.

EndNote

Öztürk Ö, Şahin Ü (01 Mart 2009) Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. Medical Journal of Süleyman Demirel University 16 1 39–47.

IEEE

[1]Ö. Öztürk ve Ü. Şahin, “Pulmoner arteriyel hipertansiyon: tanı ve tedavisi”, SDÜ Tıp Fak Derg, c. 16, sy 1, ss. 39–47, Mar. 2009, doi: 10.17343/sdutfd.36555.

ISNAD

Öztürk, Önder - Şahin, Ünal. “Pulmoner arteriyel hipertansiyon: tanı ve tedavisi”. Medical Journal of Süleyman Demirel University 16/1 (01 Mart 2009): 39-47. https://doi.org/10.17343/sdutfd.36555.

JAMA

1.Öztürk Ö, Şahin Ü. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. SDÜ Tıp Fak Derg. 2009;16:39–47.

MLA

Öztürk, Önder, ve Ünal Şahin. “Pulmoner arteriyel hipertansiyon: tanı ve tedavisi”. Medical Journal of Süleyman Demirel University, c. 16, sy 1, Mart 2009, ss. 39-47, doi:10.17343/sdutfd.36555.

Vancouver

1.Önder Öztürk, Ünal Şahin. Pulmoner arteriyel hipertansiyon: tanı ve tedavisi. SDÜ Tıp Fak Derg. 01 Mart 2009;16(1):39-47. doi:10.17343/sdutfd.36555