Kistik Nefroma Tanısı Alan 19 Aylık Kız Olgu

Abstract

Kistik nefroma, böbreğin iyi huylu kistik tümörü olup, genelde tek taraflı böbrek tutulumu ile tanı alır. Tipik olarak renal parankimden kaynaklanan kistik nefroma, sıklıkla nefrektomi ile tedavi edilir. Üç ay ile iki yaş arasında, genelde erkeklerde saptanır. Bu yazıda, klinik ve radyolojiyle sağ böbrekte multiloküler kistik kitle saptanan, sağ total nefrektomi ile kistik nefroma tanısı alan, 19 aylık kız olgu sunuldu. Olgunun, histopatolojik tanısı tamamen kistik nefroma ile uyumlu saptandı. İnfantil dönemde tek taraflı kistik kitle bulunan olgularda, kistik nefroma da ayırıcı tanılar içinde düşünülmelidir.

Keywords

• Böbrek, Çocuk, Kist, Nefrektomi

A 19-Month-Old Girl Diagnosed with Cystic Nephroma

Abstract

Cystic nephroma is a rare benign cystic tumour of the kidney and is usually diagnosed with unilateral involvement. It typically arises from the renal parenchyma and is often treated with nephrectomy. It is usually detected in males between 3 months and 2 years of age. In this article, we present a case report of 19-month-old girl who presented with a cystic mass in the right kidney found by clinical and imaging techniques and underwent right total nephrectomy. The pathologic examination confirmed a cystic nephroma. In conclusion, cystic nephroma should be considered in the differential diagnosis when an infant has a unilateral cystic kidney

Keywords

• Kidney, Child, Cyst, Nephrectomy

References

1. Lenz MP, Warmann SW, Scheel-Walter HG, Schäfer J, Wehrmann M, Hacker HW, et al. A complicated case of bilateral cystic nephroma in a 16-month-old boy. Pediatr Surg Int 2005;21: 1011-4.
2. Kuzgunbay B, Turunc T, Bolat F, Kilinc F. Adult cystic nephroma: A case report and a review of the literature. Urol Oncol 2009;27: 407-9.
3. Dong B, Wang Y, Zhang J, Fu Y, Wang G. Multilocular cystic nephroma treated with laparoscopic nephron-sparing surgery: A case report. Can Urol Assoc J 2014;8:E545-7.
4. Dell’Atti L. An unusual presentation of cystic nephroma in an adult man. Rare Tumors 2015;7:58-60.
5. Babu S, Agarwal R, Narayansamy K, Rajendranath R, Balasubramanian S. Cystic renal neoplasm causing hypertension in a 2-year-old child. Saudi J Kidney Dis Transpl 2011;22:779-81.
6. Bouhafs A, Cherradi N, Lamaalmi N, Belkacem R, Barahioui M. An unusual case of multilocular cystic nephroma with prominent renal pelvis involvement. Int J Urol 2006;13:436-8.
7. Şen S. Üro-onkoloji ve böbreğin kistik lezyonları. Üroonkoloji Bülteni 2007;1:7-16.
8. Luithle T, Szavay P, Furtwängler R, Graf N, Fuchs J; SIOP/GPOH Study Group. Treatment of cystic nephroma and cystic partially differentiated nephroblastoma-a report from the SIOP/GPOH study group. J Urol 2007;177:294-6.

9. Tang TT, Harb JM, Oechler HW, Camitta BM. Multilocular renal cyst: Electron microscopic evidence of pathogenesis. Am J Pediatr Hematol Oncol 1984;6:27-32.