Kistik Nefroma Tanısı Alan 19 Aylık Kız Olgu

Öz

Kistik nefroma, böbreğin iyi huylu kistik tümörü olup, genelde tek taraflı böbrek tutulumu ile tanı alır. Tipik olarak renal parankimden kaynaklanan kistik nefroma, sıklıkla nefrektomi ile tedavi edilir. Üç ay ile iki yaş arasında, genelde erkeklerde saptanır. Bu yazıda, klinik ve radyolojiyle sağ böbrekte multiloküler kistik kitle saptanan, sağ total nefrektomi ile kistik nefroma tanısı alan, 19 aylık kız olgu sunuldu. Olgunun, histopatolojik tanısı tamamen kistik nefroma ile uyumlu saptandı. İnfantil dönemde tek taraflı kistik kitle bulunan olgularda, kistik nefroma da ayırıcı tanılar içinde düşünülmelidir.

Anahtar Kelimeler

• Böbrek, Çocuk, Kist, Nefrektomi

A 19-Month-Old Girl Diagnosed with Cystic Nephroma

Öz

Cystic nephroma is a rare benign cystic tumour of the kidney and is usually diagnosed with unilateral involvement. It typically arises from the renal parenchyma and is often treated with nephrectomy. It is usually detected in males between 3 months and 2 years of age. In this article, we present a case report of 19-month-old girl who presented with a cystic mass in the right kidney found by clinical and imaging techniques and underwent right total nephrectomy. The pathologic examination confirmed a cystic nephroma. In conclusion, cystic nephroma should be considered in the differential diagnosis when an infant has a unilateral cystic kidney

Anahtar Kelimeler

• Kidney, Child, Cyst, Nephrectomy

Kaynakça

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