Anesthesia Management Of A Patient With Neurofibromatosis

Year 2016, Volume: 8 Issue: 2, 75 - 78, 24.07.2016

Hakan Bayır

Abstract

Neurofibromatosis is an autosomal dominant and multisistemic disorder characterized by the formation of tumours. There are two types of Neurofibromatosis (NF); NF1 and NF2. NF 1 is more commonly seen and neurofibromas can be found in multiple systems. In this case report, anesthetic management of neurofibromatosis was reviewed in a patient with neurofibroma extending from L1 vertebrae to the sacrum in the lumbar region.

Keywords

Neurofibromatosis, general anesthesia, neurofibroma

Nörofîbromatozisli Hastada Anestezi Yönetimi

Abstract

Nörofibromatozis, otozomal dominant geçişli, tümöral oluşumla karakterize multi-sistemik bir hastalıktır. NF1 ve NF2 olarak iki tipi vardır. NF 1 daha sık görülüp, nö-rofibromlar birden fazla sistemde bulunabilir. Genel anestezi ve rejyonel anestezi uygulaması bu hastalarda özellik taşır. Bu olgu sunumunda, bel bölgesinde L1 ver-tebradan sakruma kadar uzanan büyüklükteki nörofibromla beraber tüm vücudunda yaygın nörofibromları olan olguda nörofibromatozisde anestezi yönetimi gözden geçirildi.

Dr. Hakan BAYIR
Dr. Recai DAĞLI
Dr. Nazan KOCAOGLU
Dr. İsa YILDIZ

Keywords

Nörofibromatozis, genel anestezi, nörofibrom

References

• 1. Hirsch NP, Murphy A, Radcliffe JJ. Neurofibromatosis: clinical presentations and anaesthetic implications. Br J Ana-esth 2001;86:555-64.
• 2. Korf BR. Neurocutaneous syndromes: Neurofibromatosis 1, neurofibromatosis 2, and tuberous sclerosis. Curr Opin Neurol 1997;10:131-6.
• 3. Bozkurt M, Yücetaş A, Kapı E, Kılınç N. Nörofibromatozisten öğrenilecek Bir Ders: Kanama Kontrolü. Türk Plastik Rekonstrüktif Ve Estetik Cerrahi Derneği 2006;14:197-9.
• 4. İnan N, Başar H, Türkoğlu M, Güleç H, Tezer E, Baltacı B. The Anesthetic Approach in a Patient with Type I Neurofib- romatosis with Multiple Deformities. Turk J Med Sci 2008;38:477-80.
• 5. Taş N, Yılmaz S. Anesthetic approach in a patient with neurofibromatozis. Journal of Experimental and Clinical Medicine 2009;26:202-5.
• 6. Esler M.D, Durbridge J, Kirby S. Epidural haematoma after dural puncture in a parturient with neurofibromatosis. Br J Anaesth 2001;87:932-4.
• 7. Thakkar SD, Feigen U, Mauther VF. Spinal tumours in neurofibromatosis type I: an MRI study of frequency, multiplicity and variety. Neuroradiology 1999;41: 625-9.
• 8. Desai A, Carvalho B, Hansen J, Hill J. Ultrasound-guided popliteal nerve block in a patient with malignant degeneration of neurofibromatosis 1. Case Rep Anesthesiol 2012;2012:1-4.
• 9. Zencirci B. Safe performance of spinal anesthesia in a critical patient with neurofibromatosis, pectus carinatum, and temporomandibular joint dysfunction: A case report. Patient Saf Surg 2010;4:7.
• 10. Dodge TL, Mahaffey JE, Thomas JD. Th anesthetic management of a patient with an obstructing intratracheal mass: a case report. Anesth Anal 1977;56: 295-8.