An exceptional survival term in primary neuroendocrine carcinoma of the vagina
Abstract
Introduction: Primary vaginal malignant tumors are rare, especially neuroendocrine tumors. The primary small cell carcinoma of the vagina is an aggressive tumor with poor prognosis because of early recurrence and metastasis.
Aim: to report the complexity of treatment of primary neuroendocrine carcinoma of vagina, and its metastasis.
Material &methods: we report a retrospective case of primary neuroendocrine carcinoma of vagina treated in our institution.
Results: We report a case of a 37-year-old woman who was diagnosed with a small cell carcinoma of the vagina without distant metastasis. The primary vaginal tumor was treated by surgery, brachytherapy, and chemotherapy. The first recurrence appeared seven years after initial diagnosis, which was a pulmonary metastasis, treated surgically. Seven years after this recurrence, she was treated with chemotherapy and surgery for another pulmonary metastasis. Fifteen years after the initial diagnosis, the patient underwent surgery for brain metastasis. She died eighteen months after the third recurrence.
Conclusions: This case splendidly illustrates a long survival term of a tumor known with poor prognosis.
Keywords
References
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Details
Primary Language
English
Subjects
-
Journal Section
Case Report
Authors
Malek Bouhani
*
0000-0001-5913-911X
Tunisia
Zemni İnes
This is me
Tunisia
Yasmine Ayari
This is me
Tunisia
Mohamed Amine Bouida
This is me
Tunisia
Riadh Chargui
This is me
Tunisia
Khaled Rahal
This is me
Publication Date
December 6, 2019
Submission Date
April 7, 2019
Acceptance Date
August 1, 2019
Published in Issue
Year 2018 Volume: 21 Number: 1