Situs inversus totalisli bir olguda spontan koroner arter diseksiyonuna bağlı ani ölüm

Öz

Situs inversus totalis, iç organların karakteristik olarak normal lokalizasyonlarının ayna görüntüsünde olduğu bir konjenital anomalidir. Asemptomatik olabilir ve normal yaşamla uyumlu olabilir. Konjenital kardiyak anomaliler eşlik edebilir. Amacımız aniden ölen 31 yaşındaki kadında tesadüfi bir situs inversus totalis olgusu bildirmektir. Otopside, situs inversus totalis ile spontan koroner arter diseksiyonunun bir arada bulunduğunu görülmüştür. Yapılan literatür taramasında situs inversus totalis’in spontan koroner arter diseksiyonu ile birlikteliği daha önce bildirilmemiştir.

Anahtar Kelimeler

• Ani ölüm
• koroner arter diseksiyonu
• situs inversus totalis
• dekstrokardi

Sudden death due to spontaneous coronary artery dissection in a case with situs inversus totalis

Öz

Situs inversus totalis is a congenital anomaly in which the visceral organs are characterically in the mirror image of their normal localisations. It can be asymptomatic and compatible with normal life. Congenital cardiac anomalies can be seen in this condition. Our aim is to report an incidental finding of situs inversus totalis in a 31-year-old female with sudden death. Autopsy studies showed that the coexistence of situs inversus totalis and spontaneous coronary artery dissection. As much as we know, the coexistence of situs inversus totalis with spontaneous coronary artery dissection has not been reported before.

Anahtar Kelimeler

• Sudden death
• coronary artery dissection
• situs inversus totalis
• dextrocardia

Kaynakça

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