Araştırma Makalesi
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Situs inversus totalisli bir olguda spontan koroner arter diseksiyonuna bağlı ani ölüm

Yıl 2021, Cilt: 35 Sayı: 2, 82 - 85, 31.08.2021
https://izlik.org/JA24ML49ER

Öz

Situs inversus totalis, iç organların karakteristik olarak normal lokalizasyonlarının ayna görüntüsünde olduğu bir konjenital anomalidir. Asemptomatik olabilir ve normal yaşamla uyumlu olabilir. Konjenital kardiyak anomaliler eşlik edebilir. Amacımız aniden ölen 31 yaşındaki kadında tesadüfi bir situs inversus totalis olgusu bildirmektir. Otopside, situs inversus totalis ile spontan koroner arter diseksiyonunun bir arada bulunduğunu görülmüştür. Yapılan literatür taramasında situs inversus totalis’in spontan koroner arter diseksiyonu ile birlikteliği daha önce bildirilmemiştir.

Kaynakça

  • Lin AE, Krikov S, Riehle-Colarusso T, Frias JL, Belmont J, Anderka M, Geva T, Getz KD, Botto LD. Laterality defects in the national birth defects prevention study 1998-2007 : birth prevalence and descriptive epidemiology. Am J Med Genet A ;164A:2581-91.
  • Ayl sworth AS. Clinical aspects of defects in the determination of laterality. Am J Med Genet 2001;101 4 :345-55.
  • Kim DK, Lee JM, Heo SY, Jung JP, Park CR, Lee YJ, Lee SC, Hwang SK, Kim GS. Acute Type A Aortic Dissection in a Patient with Situs Inversus Totalis. Korean J Thorac Cardiovasc Surg. ;53 5 :321-323. doi: 10.5090/kjtcs.20.006.
  • Gilhofer TS, Saw J. Spontaneous coronary artery dissection: update 2019. Curr Opin Cardiol. 2019;34 6 :594-602.
  • Dutta M, Sarma J. Situs inversus totalis - a case report. Natl J Clin Anat 2014;3:220-4
  • Yip A, Saw J. Spontaneous coronary artery dissection-A re- view. Cardiovasc Diagn Ther. 2015;5 1 :37-48.
  • Saw J, Mancini GB, Humphries K, Fung A, Boone R, Staro- voytoy A, Aymong E. Angiographic appearance of spontaneous coronary artery dissection with intramural hematoma proven on intracoronary imaging. Catheter Cardiovasc Interv 2016; 87:E54– E61.
  • Tweet MS, Eleid MF, Best PJ, Lennon RJ, Lerman A, Rihal CS, Holmes JR DR, Hayes SN, Gulati R. Spontaneous coronary artery dissection: revascularization versus conservative therapy. Circ Cardiovasc Interv 2014;7:777–86.
  • Rashid HN, Wong DT, Wijesekera H, Gutman S, Shanmugam VB, Gulati R, Malaipan Y, Meredith IT, Psaltis PJ.
  • Saw J. Coronary angiogram classification of spontaneous coronary artery dissection. Catheter Cardiovasc Interv 2014; :1115-22.
  • Saw J, Aymong E, Sedlak T, Buller CE, Starovoytov A, Ricci D, Robinson S, Vuurmans T, Gao M, Humphries K, John Man- cini GB. Spontaneous coronary artery dissection: association with predisposing arteriopathies and precipitating stressors and cardiovascular outcomes. Circ Cardiovasc Interv 2014; 7:645-55.
  • Lettieri C, Zavalloni D, Rossini R, Morici N, Ettori F, Leonzi O, Latib A, Ferlini M, Trabattoni D, Colombo P, Galli M, Tarantini G, Napodano M, Piccaluga E, Passamonti E, Sganzerla P, Ielasi A, Coccato M, Martinoni A, Musumeci G, Zanini R, Castiglioni B. Management and long-term prognosis of spontaneous coronary artery dissection. Am J Cardiol 2015; 116:66-73.
  • Pretty H. Dissecting aneurysm of coronary artery in a woman aged 42: rupture. BMJ 1931; 1:667.
  • Saw J, Mancini GBJ, Humphries KH. Contemporary review on spontaneous coronary artery dissection. J Am Coll Cardiol ; 68:297-312.
  • Gilhofer TS, Saw J. Spontaneous coronary artery dissection: a review of complications and management strategies. Expert Rev Cardiovasc Ther 2019; 17:275-91.
  • Melez İE, Arslan MN, Melez DO, Akçay A, Büyük Y, Avşar A, Kumral B, Şirin G, Karayel FA, Daş T, Dokudan YE, Şam B. Spon- taneous Coronary Artery Dissection: Report of 3 Cases and Lit- erature Review Hormonal, Autoimmune, Morphological Factors. Am J Forensic Med Pathol. 2015 ;36 3 :188-92.

Sudden death due to spontaneous coronary artery dissection in a case with situs inversus totalis

Yıl 2021, Cilt: 35 Sayı: 2, 82 - 85, 31.08.2021
https://izlik.org/JA24ML49ER

Öz

Situs inversus totalis is a congenital anomaly in which the visceral organs are characterically in the mirror image of their normal localisations. It can be asymptomatic and compatible with normal life. Congenital cardiac anomalies can be seen in this condition. Our aim is to report an incidental finding of situs inversus totalis in a 31-year-old female with sudden death. Autopsy studies showed that the coexistence of situs inversus totalis and spontaneous coronary artery dissection. As much as we know, the coexistence of situs inversus totalis with spontaneous coronary artery dissection has not been reported before.

Kaynakça

  • Lin AE, Krikov S, Riehle-Colarusso T, Frias JL, Belmont J, Anderka M, Geva T, Getz KD, Botto LD. Laterality defects in the national birth defects prevention study 1998-2007 : birth prevalence and descriptive epidemiology. Am J Med Genet A ;164A:2581-91.
  • Ayl sworth AS. Clinical aspects of defects in the determination of laterality. Am J Med Genet 2001;101 4 :345-55.
  • Kim DK, Lee JM, Heo SY, Jung JP, Park CR, Lee YJ, Lee SC, Hwang SK, Kim GS. Acute Type A Aortic Dissection in a Patient with Situs Inversus Totalis. Korean J Thorac Cardiovasc Surg. ;53 5 :321-323. doi: 10.5090/kjtcs.20.006.
  • Gilhofer TS, Saw J. Spontaneous coronary artery dissection: update 2019. Curr Opin Cardiol. 2019;34 6 :594-602.
  • Dutta M, Sarma J. Situs inversus totalis - a case report. Natl J Clin Anat 2014;3:220-4
  • Yip A, Saw J. Spontaneous coronary artery dissection-A re- view. Cardiovasc Diagn Ther. 2015;5 1 :37-48.
  • Saw J, Mancini GB, Humphries K, Fung A, Boone R, Staro- voytoy A, Aymong E. Angiographic appearance of spontaneous coronary artery dissection with intramural hematoma proven on intracoronary imaging. Catheter Cardiovasc Interv 2016; 87:E54– E61.
  • Tweet MS, Eleid MF, Best PJ, Lennon RJ, Lerman A, Rihal CS, Holmes JR DR, Hayes SN, Gulati R. Spontaneous coronary artery dissection: revascularization versus conservative therapy. Circ Cardiovasc Interv 2014;7:777–86.
  • Rashid HN, Wong DT, Wijesekera H, Gutman S, Shanmugam VB, Gulati R, Malaipan Y, Meredith IT, Psaltis PJ.
  • Saw J. Coronary angiogram classification of spontaneous coronary artery dissection. Catheter Cardiovasc Interv 2014; :1115-22.
  • Saw J, Aymong E, Sedlak T, Buller CE, Starovoytov A, Ricci D, Robinson S, Vuurmans T, Gao M, Humphries K, John Man- cini GB. Spontaneous coronary artery dissection: association with predisposing arteriopathies and precipitating stressors and cardiovascular outcomes. Circ Cardiovasc Interv 2014; 7:645-55.
  • Lettieri C, Zavalloni D, Rossini R, Morici N, Ettori F, Leonzi O, Latib A, Ferlini M, Trabattoni D, Colombo P, Galli M, Tarantini G, Napodano M, Piccaluga E, Passamonti E, Sganzerla P, Ielasi A, Coccato M, Martinoni A, Musumeci G, Zanini R, Castiglioni B. Management and long-term prognosis of spontaneous coronary artery dissection. Am J Cardiol 2015; 116:66-73.
  • Pretty H. Dissecting aneurysm of coronary artery in a woman aged 42: rupture. BMJ 1931; 1:667.
  • Saw J, Mancini GBJ, Humphries KH. Contemporary review on spontaneous coronary artery dissection. J Am Coll Cardiol ; 68:297-312.
  • Gilhofer TS, Saw J. Spontaneous coronary artery dissection: a review of complications and management strategies. Expert Rev Cardiovasc Ther 2019; 17:275-91.
  • Melez İE, Arslan MN, Melez DO, Akçay A, Büyük Y, Avşar A, Kumral B, Şirin G, Karayel FA, Daş T, Dokudan YE, Şam B. Spon- taneous Coronary Artery Dissection: Report of 3 Cases and Lit- erature Review Hormonal, Autoimmune, Morphological Factors. Am J Forensic Med Pathol. 2015 ;36 3 :188-92.
Toplam 16 adet kaynakça vardır.

Ayrıntılar

Birincil Dil Türkçe
Konular Adli Biyoloji
Bölüm Araştırma Makalesi
Yazarlar

Aytül Buğra Bu kişi benim

Ceyhun Küçük Bu kişi benim

Abdul Kerim Buğra Bu kişi benim

Gönderilme Tarihi 1 Ocak 2021
Yayımlanma Tarihi 31 Ağustos 2021
IZ https://izlik.org/JA24ML49ER
Yayımlandığı Sayı Yıl 2021 Cilt: 35 Sayı: 2

Kaynak Göster

Vancouver 1.Aytül Buğra, Ceyhun Küçük, Abdul Kerim Buğra. Situs inversus totalisli bir olguda spontan koroner arter diseksiyonuna bağlı ani ölüm. ATD [Internet]. 01 Ağustos 2021;35(2):82-5. Erişim adresi: https://izlik.org/JA24ML49ER

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