Hemophagocytic syndrome and fulminant hepatic failure

Öz

Hemophagocytic syndrome is a clinical manifestation of hemophagocytosis that is characterized by high fever, hepatosplenomegaly, and pancytopenia. Infections, hematological malignancies and connective tissue diseases are the main etiological factors of hemophagocytic syndrome. In this article, we present a case with fulminant hepatic failure associated with hemophagocytic syndrome.

Anahtar Kelimeler

• Hemophagocytic syndrome, hemophagocytosis, fulminant hepatic failure

Hemofagositik sendrom ve fulminan hepatit

Öz

Hemofagositik sendrom; makrofajların kan hücrelerini fagosite etmesiyle karakterize ve ateş, hepatosplenomegali, pansitopeni gibi bulgularla kendini gösteren klinik bir tablodur. Hemofagositik sendromun etyolojisinde başlıca enfeksiyonlar, hematolojik maliniteler ve bağ doku hastalı kları yer almaktadır. Bu yazıda hemofagositik sendrom ve fulminan hepatit birlikteliği gösteren bir olgu sunulmaktadır.

Anahtar Kelimeler

• Hemofagositik sendrom, hemofagositoz, fulminan hepatit

Kaynakça

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