Paroxysmal nocturnal hemoglobinuria: Due to rarely seen cause portal vein thrombosis

Yıl 2005, Cilt: 4 Sayı: 2, 135 - 138, 01.08.2005

Gönenç Kocabay Çetin Karaca Kadir Demir Engin Türkmen Betül Tiryaki Uğur Çevikbaş Fatih Beşışık Yılmaz Çakaloğlu Atilla Ökten

Öz

Portal vein thrombosis, which is seen during coagulopathies, vasculitis or myeloproliferative diseases, causes extrahepatic presinusoidal portal hypertension. Paroxysmal nocturnal hemoglobinuria usually causes thrombosis in hepatic veins, but it also rarely causes portal vein thrombosis. A case of paroxysmal nocturnal hemoglobinuria due to portal vein thrombosis is presented.

Anahtar Kelimeler

Paroxysmal nocturnal hemoglobinuria, portal vein thrombosis

Portal ven trombozunun nadir bir sebebi: Paroksismal nokturnal hemoglobinüri

Öz

Portal ven trombozu, koagülopatiler, vaskülit veya miyeloproliferatif hastalıkların seyrinde görülen, ekstrahepatik presinüzoidal portal hipertansiyon nedenidir. Paroksismal nokturnal hemoglobinüri, daha çok hepatik venlerde tromboza neden olmakla birlikte, portal ven trombozunun nadir nedenleri arasındadır. Burada sebebi paroksismal nokturnal hemoglobinüri olan bir portal ven trombozu olgusu sunuldu.

Anahtar Kelimeler

Paroksismal nokturnal hemoglobinuri, portal ven trombozu

Kaynakça

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