Rare Tumors of the Lung; 74 Cases

Abstract

Objective: We aimed to evaluate the rare tumors of the lung in a single article in this study. Thus, these cases, which were included in the literature as case reports, were collected under a single article.Material and Methods: In this retrospective study 6879 patients who were operated between January 2010 and December 2017 in our clinic. In the histological classification, tumors with an incidence of less than 5% were accepted as rare tumors. 74 cases of a rare tumor of the lung were examined by subgroups.Results: The average age of 74 patients in the study was 54.5 years. Twelve of the patients were female and 62 were male. While 83.3% of the patients with a diagnosis of tumorlet were female, 100% of patients with a diagnosis of large cell neuroendocrine tumor was male.Eighteen of the 74 patients included in the study had died and 56 were being followed up and treated.Conclusion: The rare tumors of the lung are usually presented in the literature as case reports and there is no definitive treatment protocol. Large series of patients are needed for better understanding of these tumors

Keywords

• Surgery, Thorax, Tumor

Akciğerin Nadir Tümörleri; 74 Olgu

Öz

Amaç: Bu çalışmada, akciğerin nadir görülen tümörlerinin birlikte değerlendirilmesi amaçlandı. Böylelikle olgu sunumları şeklinde literatürde yer alan bu olgular tek bir yazı altında toplanmaya çalışıldı. Gereç ve Yöntemler: Bu geriye dönük çalışmaya kliniğimizde Ocak 2010 ile Aralık 2017 tarihleri arasında opere edilen 6879 hasta dahil edildi. Histolojik sınıflamada, görülme sıklığı %5ʼden az olan tümörler nadir tümör olarak kabul edildi. Akciğerin nadir tümörü tanısı alan 74 olgu alt gruplara ayrılarak incelendi. Bulgular: Çalışmadaki 74 hastanın yaş ortalaması 54,5’dir. Hastaların 12 tanesi kadın 62 tanesi erkekti. Tümörlet tanısı alan olguların, %83,3’ü kadın iken büyük hücreli nöroendokrin tümör tanısı alan olguların %100’ü erkekti. Araştırmaya dâhil edilen 74 hastanın 18 tanesi eksitus olurken, 56 tanesinin takip ve tedavileri devam etmektedir.Sonuç: Akciğerin nadir tümörleri literatürde genellikle olgu sunumları şeklinde bulunmaktadır ve kesinleşmiş bir tedavi protokolleri yoktur. Bu tümörlerin daha iyi anlaşılabilmesi için geniş hasta serilerine ihtiyaç vardır

Anahtar Kelimeler

• Cerrahi, Toraks, Tümör

Kaynakça

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