Anesthesia management of a pediatric patient with Wolf-Hirschhorn Syndrome: A case report
Öz
Wolf-Hirschhorn syndrome (WHS) is a rare chromosomal anomaly caused by the deletion of the short arm of chromosome 4. The leading causes of death are aspiration pneumonia, epilepsy, and infection. In this study, we aimed to present our anesthesia experience in a patient with WHS who was scheduled for cleft palate surgery and in whom we performed total intravenous anesthesia (TIVA).
In the clinical examination of our 8-year-old patient with WHS, weighing 13 kg, who was planned to undergo cleft palate surgery. Growth retardation, cleft palate, micrognathia, epicanthus and hyptonia were present. Anesthesia induction was performed with 1 mg/kg i.v lidocaine, 2 mg/kg i.v propofol and 1 mg/kg i.v fentanyl, 0.5 mg/kg i.v rocuronium bromide. TIVA (0.5 µg/kg/min remifentanil and 75 µg/kg/min propofol i.v) was used for maintenance of anesthesia. In the perioperative period, the pulse rate was 170 beats/min for a short time. Extubation was achieved 13 minutes after the end of surgery.
We think that TIVA (Propofol, remifentanil) and C-MAC videolaryngoscope as intubation device is a reliable method in the anesthetic management of children with WHS syndrome.
Anahtar Kelimeler
Airway management, anesthesia, laryngoscope, Wolf-Hirschhorn syndrome
Destekleyen Kurum
yok
Etik Beyan
Financial Resource
No financial resources were used for this article.
Conflict of Interest
There is no conflict of interest regarding this article.
Teşekkür
yok
Kaynakça
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