Incomplete Cantrell Pentalogy Diagnosis Case Report

Yıl 2023, Cilt: 12 Sayı: 2, 441 - 444, 23.06.2023

Mahmut Serkan Sarıkaya , İpek Dokurel , Orkun Çetin , Tümerkan Cenk

https://doi.org/10.53424/balikesirsbd.1055769

Öz

Cantrell pentalogy is a rare disorder encountered in fetal an intrauterine life. Pentalogy of Cantrell consist more than one pathological components these are sternal, pericardial, diafragmatic, anterior abdominal wall defects.Pentalogy of Cantrell firstly described by Cantrelll and colleageus at 1958. Prevalance of Cantrell is 1/65.000- 1/200.000. In our case we want to evaluate clinical and post clinical pathways insight of literature.

Anahtar Kelimeler

Cantrell, incomplete, prognosis

İnkomplet Cantrell Pentolojisi Tanı Olgu Sunumu

Öz

Cantrell Pentalojisi, intrauterin ve fetal hayatta karşılaşılan birden fazla doğumsal defektin yer aldığı nadir bir konjenital hastalıktır. Pentalojinin içinde sternal, perikardiyal ,diafragmatik ,kardiyak ve karın ön duvarı patolojileri bulunmaktadır. Cantrell pentalojisinin prevelansı 1/65.000-1/200.000 arasında olup 1958 yılında Cantrell ve arkadaşları tarafından tanımlanmıştır. Olgumuzda birinci trimesterde prenatal tanısı konulan Cantrell pentalojisi olgusunu literatür bilgileri ile beraber tanı ve sonrası için yapılanları değerlendirdik.

Anahtar Kelimeler

Cantrell, inkomplet, prognoz

Kaynakça

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• Toyama, W. M. (1972). Combined congenital defects of the anterior abdominal wall, sternum, diaphragm, pericardium, and heart: a case report and review of the syndrome. Pediatrics, 50(5), 778-792. https://doi.org/10.1542/peds.50.5.778
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