Prolonged Compilation Due to Rett Syndrome: Case Report

Öz

Rett Sendromu, zeka geriliği, nöbetler, hareket bozukluğu, otistik davranış ve anormal solunum yolu örneği gibi nörolojik belirtilere eşlik eden X bağlantılı bir kalıtsal hastalıktır. Anesteziyologlar için perioperatif dönemde skolyoz mikrognati ve buna bağlı solunum problemleri nedeniyle entübasyon zorluğu ve anormal solunum yolu paternine bağlı önemli bir klinik tablo. Bu olgu sunumunda, Rett Sendromu ve anestezik yaklaşımdan dolayı bu vakalarda uzun süreli derlemeyi sunmak istiyoruz.

Anahtar Kelimeler

• RETT sendromu,genişletilmiş derleme,genel anestezi

Prolonged Compilation Due to Rett Syndrome: Case Report

Öz

Rett Syndrome is a X-linked hereditary disease, accompanying neurological manifestations such as mental retardation, seizures, movement disorder, autistic behavior and abnormal respiratory pattern. It is an important clinical picture for anesthesiologists during perioperative period due to scoliosis and related respiratory problems, intubation diffi culty due to micrognathia and abnormal respiratory pattern. In this case report we would like to present prolonged compilation due to Rett Syndrome and anesthetic approach in these cases.

Anahtar Kelimeler

• RETT syndrome,extended compilation,general anesthesia

Kaynakça

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