VENA KAVA SÜPERİOR SENDROMUYLA TANI ALAN YÜKSEK DERECELİ NÖROENDOKRİN KARSİNOM: OLGU SUNUMU

Yıl 2020, Cilt: 7 Sayı: 2, 243 - 246, 30.06.2020

Nagihan Kolkıran , Gamze Göksel , Ferhat Ekinci Atike Pınar Erdoğan , Ahmet Dirican , Cihan Göktan

https://doi.org/10.34087/cbusbed.575496

Öz

   Nöroendokrin
tümörler başta akciğer ve gastrointestinal sistem olmak üzere tüm vücutta
görülebilen nadir tümörlerdir.(1,2) 
Akciğer karsinomlarının %20 ‘sini oluşturur.(1,2) Akciğer nöroendokrin
tümörlerde vena kava süperior sendromu (VKSS) sıklığı bilinmemektedir. İntratorasik
maligniteler VKSS’nin %60-%85’inden sorumludur ve tümör tanısı önceden konulmamış
bu olguların %60 ‘ı vena kava superior obstrüksiyonu ile prezente olur. Bu
olgularda venöz obstrüksiyon; vena kava süperiora primer tümörün, mediastinal
lenf nodlarının dıştan basısı veya  direk
tümör invazyonu sonucunda meydana gelir. Literatürde sağkalım verileri olgu
sunumu düzeyinde olmakla birlikte tedavisiz kalan olgularda sağkalım 1 ay
civarında bildirilmektedir. Bu nedenle hızlı tanı konulup uygun tedavinin
planlanması hayati önem taşımaktadır. Burada akciğer nöroendokrin tümör
nedeniyle VKSS gelişen olgunun tanısal süreci ve prognozu sunulmuştur.

Anahtar Kelimeler

Vena kava superior sendromu , nöroendokrin tümör , tedavi

Kaynakça

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