Idiopathic Hypoparathyroidism associated Fahr's Disease: Two Case Reports and Review of the Literature
Öz
Bilateral Striopallidodentat Calcinosis also called Fahr's disease (FH); basal ganglia, thalamus, and cerebellar dentate nucleus is a disease characterized by symmetric calcifications in the cerebral white matter. Calcifications are often drawn attention in brain imaging for other reasons. The disease can progress with clinically variable neurological or neuro-psychiatric symptoms. Fahr's disease are believed to be associated with anoxia, radiation, systemic diseases, toxins calcium metabolism disorders, and encephalitis. We presented two cases with primary hypoparathyroidism were diagnosed and detected of neurological problems, cerebral and cerebellar calcifications on imaging.
Anahtar Kelimeler
Kaynakça
- Ellie E, Julien J, Ferrer X. Familial idiopathic striopallidodentate calcifications. Neurology. 1989;39:381-5.
- Modrego PJ, Mojonero J, Serrano M, Fayed N. Fahr’s syndrome presenting with pure and progressive presenile demantia. Neurol Sci. 2005;26:367–9.
- Malik R, Pandya VK, Naik D. Fahr disease. A rare neurodegenerative disorder. Ind J Radiol Imag. 2004;14:383-4.
- Özkur A, Şirikci A, Bayram M. Fahr hastalığı: BT
- bulguları.Türk Tanısal ve Girişimsel Radyoloji Dergisi. 2001;7:142-3.
- Bala V, Mohit BH, William DM. Bilateral Striopallidodentate Calcinosis: Cerebrospinal Fluid, Imaging and Electro physiological studies. Annals of Neurology. 1992;31:379-84.
- Smeyers VJ, Michotte Y. Pelsmaeckers J, Loventhal A, et al. The chemical composition of idiopathic nonarteriosclerotic cerebral calcifications. Neurology. 1975;25:48-57.
- Geschwind DH, Loginov M, Stern JM. Identification of a locus on chromosome 14q for idiopathic basal ganglia calcification (Fahr disease). Am J Hum Genet. 1999;65:764–72.
- Koçak S, Erdemir E, Bayrak A, Kara H, Gül M. Fahr Hastalığı: İki Olgu Sunumu. Akademik Acil Tıp Dergisi (JAEM). 2009;8:4
- El Maghraoui A, Birouk N, Zaim A, Slassi I, Yahyaoui M, Chkili T. Fahr Syndrome and dysparathyroidism. 3 cases. 1995;24:1301-4. Presse Med.
