A Rare Case Presenting with Symptoms of Familial Pheochromacytoma

Yıl 2015, Cilt: 40 Sayı: 3, 593 - 596, 30.09.2015

Mehtap Evran , Gamze Akkuş Murat Sert Tamer Tetiker

https://doi.org/10.17826/cutf.81730

Öz

Pheochromocytoma is a rare tumor in which seen an incidence of 1 per 100.000 in the general population. Pheochromocytoma is a catecholamine producing neuroendocrine tumor arising from adrenal medulla. A 46-year-old man experienced headache, sweating and palpitation referred to our hospital. Familial pheocromocytoma was detected. We presented this case as whole family members had suffered from morbidities and deaths due to this disorder

Anahtar Kelimeler

Pheocromocytoma, familial disorder, hypertension

Familyal Feokromasitoma Semptomlarıyla Başvuran Nadir Bir Olgu

Öz

Feokromasitoma 100.000 kişide bir görülebilen nadir tümörlerden birisidir. Genel olarak adrenal medulladan katekolamin salınımı ile karakterizedir. Kırk altı yaşında erkek hasta baş ağrısı, terleme, çarpıntı şikayeti ile kliniğimize başvurdu. Hastaya feokromasitoma tanısı konuldu. Bu yazıda ailesinde feokromasitomaya bağlı morbidite ve ölüm öyküsü olan bir hasta aktarılmıştır.

Anahtar Kelimeler

Feokromasitoma, ailesel hastalık, hipertansiyon

Kaynakça

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