Two Oligodontia Cases Without Genetic Anomaly

Öz

Although congenital tooth agenesis is a common dental finding, oligodontia is a rare developmental dental anomaly associated with tooth number. Oligodontia, defined as the congenital absence of six or more teeth. Excluding the third molars, is commonly associated with syndromes and systemic abnormalities. Genetic factors may play an important role in oligodontia which may occur as part of a syndrome or as an isolated finding. This report presents two cases of oligodontia, 19 and 15 years, made certain after genetic consultation not to be associated with any syndromes or systemic abnormalities. In the first case only 16 teeth were present in the mouth and most of their shapes were microdont. In the intra oral examination of the second case only 5 permanent teeth were deteced and the panoramic radiograph showed 23 missing permanent teeth except third molars

Anahtar Kelimeler

• Hypodontia, oligodontia, dental anomaly

GENETİK ANOMALİSİ OLMAYAN İKİ OLİGODONTİ OLGUSU

Öz

Konjenital diş eksikliği çok sık görülmesine rağmen, oligodonti nadir rastlanılan gelişimsel bir diş sayı anomalisidir. Üçüncü molar dişler sayılmaksızın, konjenital olarak altı veya daha fazla dişin eksikliği olarak tanımlanan oligodonti, genellikle sendromlar ve sistemik anomaliler ile ilişkilidir. Oligodontide genetik faktörler sendromların bir parçası olarak veya tek başına bir bulgu olarak önemlidir. Çalışmada, genetik değerlendirme sonucu herhangi bir sendromla ilişkili olmadığı saptanan 15 ve 19 yaşlarındaki iki oligodonti olgusu sunulmaktadır. Olgulardan birinde ağızda sadece 16 adet diş bulunduğu ve bu dişlerin çoğunun mikrodonti şeklinde olduğu belirlendi. İkinci olgunun yapılan intraoral muayenesinde sadece 5 adet daimi dişin mevcut olduğu gözlendi. Alınan panoramik radyograf ile üçüncü molar dişler hariç 23 adet daimi dişin eksik olduğunu tespit edildi

Anahtar Kelimeler

• Hipodonti, oligodonti, dental anomali

Kaynakça

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