Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child

Cilt: 4 Sayı: 1 27 Temmuz 2014
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Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child

Öz

Achondroplasia is the most common skeletal dysplasia in children. Achondroplasic patients often have respiratory problems associated with upper respiratory tract obstruction and craniofacial dysmorphology. Chronic hypoxemia in these patients can result in pulmonary hypertension. In this report an achondroplasic child with severe day-time pulmonary hypertension is presented.

 

 

Anahtar Kelimeler

Kaynakça

  1. Horton WA, Hall JG, Hecht JT. Achondroplasia. Lancet 2007; 370:162–172
  2. Zucconi M, Weber G, Castronovo V, Ferini-Strambi L, Russo F, Chiumello G, Smirne S. Sleep and upper airway obstruction in children with achondroplasia. J Pediatr. 1996;129(5):743-9
  3. Mogayzel PJ Jr, Carroll JL, Loughlin GM, Hurko O, Francomano CA, Marcus CL. Sleep-disordered breathing in children with achondroplasia. J Pediatr. 1998;132:667-71.
  4. Schlüter B, De Sousa G, Trowitzsch E, Andler W. Diagnostics and management of sleep-related respiratory disturbances in children with skeletal dysplasia caused by FGFR3 mutations (achondroplasia and hypochondroplasia). Georgian Med News. 2011;196-197:63-72
  5. Apprill M, Weitzenblum E, Krieger J, Oswald M, Kurtz D. Frequency and mechanism of daytime pulmonary hypertension in patients with obstructive sleep apnea syndrome. Cor Vasa. 1991;33:42-9
  6. Alchanatis M, Tourkohoriti G, Kakouros S, Kosmas E, Podaras S, Jordanoglou JB. Daytime pulmonary hypertension in patients with obstructive sleep apnea: the effect of continuous positive airway pressure in pulmonary hemodynamics. Respiration 2001;68:566-72.
  7. Sajkov D, McEvoy RD. Obstructive sleep apnea and pulmonary hypertension. Prog Cardiovasc Dis. 2009;51:363-70
  8. Adegunsoye A, Ramachandran S. Etiopathogenetic mechanisms of pulmonary hypertension in sleep-related breathing disorders. Pulm Med. 2012;2012:273591. doi: 10.1155/2012/273591. Epub 2012 Jul 11.

Ayrıntılar

Birincil Dil

İngilizce

Konular

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Bölüm

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Yayımlanma Tarihi

27 Temmuz 2014

Gönderilme Tarihi

27 Temmuz 2014

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2014 Cilt: 4 Sayı: 1

Kaynak Göster

APA
Doğan, V., Taşkın, S., Karaaslan, E., Yilmaz, R., & Çakan, N. (2014). Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child. Çağdaş Tıp Dergisi, 4(1), 41-43. https://izlik.org/JA76BD29XD
AMA
1.Doğan V, Taşkın S, Karaaslan E, Yilmaz R, Çakan N. Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child. J Contemp Med. 2014;4(1):41-43. https://izlik.org/JA76BD29XD
Chicago
Doğan, Vehbi, Sema Taşkın, Erhan Karaaslan, Resul Yilmaz, ve Nurşen Çakan. 2014. “Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child”. Çağdaş Tıp Dergisi 4 (1): 41-43. https://izlik.org/JA76BD29XD.
EndNote
Doğan V, Taşkın S, Karaaslan E, Yilmaz R, Çakan N (01 Temmuz 2014) Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child. Çağdaş Tıp Dergisi 4 1 41–43.
IEEE
[1]V. Doğan, S. Taşkın, E. Karaaslan, R. Yilmaz, ve N. Çakan, “Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child”, J Contemp Med, c. 4, sy 1, ss. 41–43, Tem. 2014, [çevrimiçi]. Erişim adresi: https://izlik.org/JA76BD29XD
ISNAD
Doğan, Vehbi - Taşkın, Sema - Karaaslan, Erhan - Yilmaz, Resul - Çakan, Nurşen. “Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child”. Çağdaş Tıp Dergisi 4/1 (01 Temmuz 2014): 41-43. https://izlik.org/JA76BD29XD.
JAMA
1.Doğan V, Taşkın S, Karaaslan E, Yilmaz R, Çakan N. Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child. J Contemp Med. 2014;4:41–43.
MLA
Doğan, Vehbi, vd. “Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child”. Çağdaş Tıp Dergisi, c. 4, sy 1, Temmuz 2014, ss. 41-43, https://izlik.org/JA76BD29XD.
Vancouver
1.Vehbi Doğan, Sema Taşkın, Erhan Karaaslan, Resul Yilmaz, Nurşen Çakan. Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child. J Contemp Med [Internet]. 01 Temmuz 2014;4(1):41-3. Erişim adresi: https://izlik.org/JA76BD29XD