Severe pulmonary hypertension due to sleep-disordered breathing in an achondroplasic child
Öz
Achondroplasia is the most common skeletal dysplasia in children. Achondroplasic patients often have respiratory problems associated with upper respiratory tract obstruction and craniofacial dysmorphology. Chronic hypoxemia in these patients can result in pulmonary hypertension. In this report an achondroplasic child with severe day-time pulmonary hypertension is presented.
Anahtar Kelimeler
Kaynakça
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Ayrıntılar
Birincil Dil
İngilizce
Konular
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Bölüm
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Yayımlanma Tarihi
27 Temmuz 2014
Gönderilme Tarihi
27 Temmuz 2014
Kabul Tarihi
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Yayımlandığı Sayı
Yıl 2014 Cilt: 4 Sayı: 1