Erişkin hastada aort koarktasyonu olgu sunumu ve literatürün gözden geçirilmesi

Öz

Aort koarktasyonu sıklıkla sol subklavian arterin distalinde aortun segmental daralması olarak tanımlanan, konjenital kalp defektlerinde %8-10 oranında görülen, izole veya diğer kardiyak defektlerle birlikte olabilen bir konjenital kalp hastalığıdır. Aortikelastisite anormallikleri ile karakterize geniş yayılımlı bir arteriyopati olarak da tanımlanmaktadır. Durum genellikle çocukluk çağında ve nadiren yetişkinlikte teşhis edilir. Yetişkinlerde en sık görülen klinik bulgu sistemik arteriyel hipertansiyondur. Bu olgu sunumunda, ekokardiyografi ve bilgisayarlı tomografi ile aort koarktasyonu tanısı konulan ve başarılı primer stent implantasyonu uygulanan, refrakter hipertansiyonu olan 39 yaşında bir kadın hastayı sunuyoruz.

Anahtar Kelimeler

• Aort koarktasyonu
• Erişkin
• Hipertansiyon

Coarctation of the aorta in an adult patient case report and review of the literature

Öz

Coarctation of the aorta is a congenital heart disease defined as a segmental narrowing of the aorta distal to the left subclavian artery. The condition is usually diagnosed in childhood and rarely in adulthood. Severe coarctation causes high mortality and heart failure in childhood, whereas adult coarctation is usually asymptomatic. The most common clinical manifestation in adults is systemic hypertension. Coarctation of the aorta is a rare cause of secondary hypertension and can lead to early death if not treated appropriately. In this case report, we present a 39-year-old woman with refractory hypertension who was diagnosed with coarctation of the aorta by echocardiography and computed tomography and underwent successful primary stent implantation.

Anahtar Kelimeler

• Coarctation of aorta
• Adult
• Hypertension

Kaynakça

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