Nadir Bir Klinik Sendrom: Median Arkuat Ligament Sendromu

Yıl 2024, , 23 - 25, 29.04.2024

Mehmet Berhuni , Hüseyin Yönder , Hasan Elkan , Abdullah Özgönül

https://doi.org/10.35440/hutfd.1386917

Öz

Özet
Amaç
Median Arkuat Ligament Sendromu (MALS), toplumda 2/100000 oranıyla oldukça nadir gözlenen bir klinik durumdur. Bu nedenle MALS olguları geç tanı alan olgulardır.
Bu yazıda, kliniğimizde MALS tanısı alan ve cerrahi tedavi uygulanan beş hastanın bulgularının literatür bilgileri eşliğinde sunulması amaçlanmıştır.
Materyal ve Metod
Kliniğimizde Ocak 2021-Aralık 2022 tarihleri arasında MALS tanısı alan ve cerrahi tedavi uygulanan beş hastanın dosyası retrospektif olarak incelenmiş ve veriler elde edilmiştir.
Bulgular
MALS tanısı ile cerrahi tedavi alan beş hasta saptandı. Hastaların üçü kadın, ikisi erkekti. Hastaların tamamında yemeklerden sonra artan karın ağrısı ve kilo kaybı şikayeti mevcuttu. Cerrahi tedavi sonrası ortalama ±13,2 (3-24 ay) aylık takiplerinde hastaların kilo aldıkları gözlendi. Ayrıca klinik şikayetlerinin de geçtiği saptandı.
Sonuç
MALS nadir görülen bir hastalık olsa da tanı ve tedavideki gecikme, hastaların kronik şikayetleri nedeniyle sağlık sistemi üzerinde yarattıkları iş gücü kaybı ve artan maliyetler nedeniyle önemlidir. Basıya neden olan fibröz bandın cerrahi tedavi ile eksizyonu, şikayetlerin giderilmesinde oldukça efektiftir.

Anahtar Kelimeler

Median Arkuat Ligament, Çölyak Arter, Karın Ağrısı

A Rare Clinical Syndrome: Median Arcuate Ligament Syndrome

Öz

Background: Median Arcuate Ligament Syndrome (MALS) is a rare clinical condition with a rate of 2/100000 in the society. Therefore, MALS cases are diagnosed late.In this article, we aimed to pre-sent the findings of five patients who were diagnosed with MALS in our clinic and underwent surgical treatment, in the light of the literature.
Materials and Methods: The files of five patients who were diagnosed with MALS and underwent surgical treatment in our clinic between January 2021 and December 2022 were reviewed retros-pectively and data were obtained.
Results: Five patients who received surgical treatment with the diagnosis of MALS were identified. Three of the patients were woman and two were man. All patients complained of weight loss and increased abdominal pain after meals. It was observed the patients gained weightin the ±13,2 (3-24) month follow-up period after the surgical treatment. In addition, it was determined that his clinical complaints were resolved.
Conclusions: Although MALS is a rare disease, it is important because of delay in diagnosis and treat-ment, loss of workforce and increasing costs on the health system due to chronic complaints of pati-ents. Surgical excision of the fibrous band thst causes the pressure, is very effective in relieving the complaints.


Key Words: Median arcuate ligament, celiac artery, abdominal pain

Kaynakça

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