Akrokeratozis verrusiformis: bir olgu sunumu Türkçe

Öz

Akrokeratozis verrusiformis otozomal dominant geçişli, nadir görülen bir genodermatozdur. Genellikle doğumda veya erken çocukluk dönemlerinde görülür. Ancak hastalığın başlaması beşinci dekata kadar gecikebilir. Akrokeratozis verrusiformis sıklıkla el ve ayak sırtlarında verruka plana benzeyen, üzeri düz, cilt renginde, çok sayıda keratotik papüllerle karakterizedir. Histopatolojisinde hiperkeratoz, akantozis ve papillomatozis saptanırken hastalık için tipik olan epidermiste 'kilise kulesi' olarak da bilinen lokalize sivri epidermal çıkıntılar görülmektedir. Burada sporadik bir akrokeratozis verrusiformis olgusu sunulmaktadır

Anahtar Kelimeler

• Akrokeratozis verrusiformis,Darier hastalığı

Acrokeratosis verruciformis: a case report

Öz

Acrokeratosis verruciformis is a rare genodermatosis with an autosomal dominant mode of inheritance. Sporadic cases can also occur, and is characterized by multiple flat-topped, skin-colored keratotic lesions resembling plane warts typically observed on the dorsum of the hands and feet. It is usually present at birth or manifests in early childhood, but the onset may be delayed until the fifth decade of life. The sections reveal hyperkeratosis, regular acanthosis, and papillomatosis with a prominent granular layer, typically having a “church spire” appearance. Herein, we aimed to report a sporodic case of acrokeratosis verruciformis

Anahtar Kelimeler

• Acrokeratosis verruciformis,Darier disease

Kaynakça

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