Hybrid approach in two cases with hypoplastic left heart syndrome

Yıl 2015, Cilt: 12 Sayı: 2, 306 - 310, 30.08.2015

Savas Demirpence Baris Guven Ali Yıldırım , Emin Alp Alayunt Vedide Tavli

Öz

Hypoplastic left heart syndrome (HLHS) encompasses a spectrum of congenital cardiac defects which
mostly include left ventricular hypoplasia or atresia, mitral valve hypoplasia or atresia and ascending aortic
hypoplasia and atresia. Hypoplastic left heart syndrome is a leading cause of neonatal mortality. In recent
years, popularity of hybrid approach has increased. Hybrid procedures which requires close cooperations
between paediatric cardiologists and cardiac surgeons includes a less invasive primary procedure;
integrating interventional cardiology approaches and surgical techniques. Herein, we report two cases with
hypoplastic left heart syndrome. We performed hybrid approach including ductal stenting and bilateral
pulmonary banding on these patients. 

Anahtar Kelimeler

Infant, newborn, hypoplastic left heart syndrome, treatment

Hibrid yaklaşımı uygulanan hipoplastik sol kalp sendromlu iki olgu

Öz

Hipoplastik sol kalp sendromu; çoğunlukla sol ventrikül hipoplazisi veya atrezisi, mitral kapak hipoplazisi
veya atrezisi ve çıkan aorta hipoplazisi veya atrezisini içeren doğumsal kalp defektleri spektrumunu kapsar.
Hipoplastik sol kalp sendromu neonatal mortalitenin önemli bir nedenidir. Son yıllarda hibrid yaklaşımın
popülaritesi artmıştır. Hibrid uygulama, pediyatrik kardiyolog ve kalp cerrahı arasında yakın işbirliği
gerektiren, girişimsel kardiyoloji yaklaşımları ve cerrahi teknikleri birleştiren ve daha az invaziv olan
birincil bir uygulamadır. Bu yazıda, hipoplastik sol kalp sendromu olan ve duktal stent ve iki taraflı pulmoner
arter bantlamayı içeren hibrid yaklaşımı uygulanan iki olguyu sunduk. 

Anahtar Kelimeler

Bebek, yenidoğan, hipoplastik sol kalp sendromu, tedavi

Kaynakça

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