Hemofagositik lenfohistiositozda santral sinir sistemi komplikasyonları

Yıl 2015, Cilt: 12 Sayı: 1, 154 - 164, 15.04.2015

Mervan Bekdaş , Sevil Bilir Göksügür , Fatih Demircioğlu

Öz

Hemofagositik lenfohistiositoz, çok sayıda sistemi etkileyen, nadir görülen bir hastalıktır. Santral sinir
sistemi tutulumu, prognozu etkilemesi ve ciddi sekel oluşturma riski nedeniyle çok önemlidir.
Hemofagositik lenfohistiositozun santral sinir sistemi tutulumu ilişkili nörolojik bulgu ve
komplikasyonların sıklıkları, özellikleri, morbidite ve mortaliteye etkisini irdeleyen yayın sayısı azdır. Bu
yazıda, hemofagositik lenfohistiositozun santral sinir sistemi tutulumu ile ilişkili klinik tabloya dikkat
çekmek istedik.

Anahtar Kelimeler

Hemofagositik lenfohistiositoz, çocuk, santral sinir sistemi

Central nervous system complications in hemophagocytic lymphohistiocytosis

Öz

Hemophagocytic lymphohistiocytosis is a rare disease, affecting multiple systems. Central nervous system
involvement is very important because of the effect on the prognosis. Arising neurological symptoms as a
result of this involvement are included in some publications, but the number of publications related to their
frequency, characteristics, and relations with morbidity and mortality is rare. In this article, we wanted to
attract attention to the picture of the central nervous system involvement as a result of hemophagocytic
lymphohistiocytosis.

Anahtar Kelimeler

Hemophagocytic lymphohistiocytosis, child, central nervous system

Kaynakça

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