Newly Diagnosed Patient with Primary Biliary Cholangitis: Case Report

Yıl 2020, Cilt: 17 Sayı: 3, 492 - 494, 25.12.2020

Nuray Kıvanç Terzi , Mehmet Sidar Güler , Dursun Çadırcı , Ahmet Uyanıkoğlu

https://doi.org/10.35440/hutfd.733455

Öz

Primary biliary cholangitis (PBC) is a slowly progressive chronic cholestatic granulomatous liver disease of unknown etiology, mostly affected by middle-aged women, accompanied by damage to the small bile ducts. PBK can cause serious diseases such as portal hypertension or liver failure and then progress to cirrhosis. As in this case, it should not be forgotten that it may come with non-specific symptoms, detailed history and diagnosis should be confirmed with necessary laboratory tests in patients suspected.

Yeni Tanı Primer Biliyer Kolanjitli Hasta: Olgu Sunumu

Öz

Primer biliyer kolanjit (PBK) etiyolojisi bilinmeyen, çoğunlukla orta yaş kadınların etkilendiği, küçük safra kanallarında hasarın eşlik ettiği, yavaş ilerleyen, kronik kolestatik granülomatöz bir karaciğer hastalığıdır. PBK, portal hipertansiyon veya karaciğer yetmezliği gibi ciddi hastalıklara neden olup sonrasında siroza ilerleyebilir. Bu vakada olduğu gibi non-spesifik semptomlarla gelebileceği unutulmamalı, ayrıntılı anamnez ve şüphelenilen hastalarda gerekli laboratuvar tetkikleri ile tanı kesinleştirilmelidir.

Anahtar Kelimeler

PBK, AMA, kaşıntı

Kaynakça

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