Yıl 2021, Cilt 7 , Sayı 1, Sayfalar 16 - 29 2021-04-30

PRADER WİLLİ SENDROMU OLAN BİREYLERDE OBEZİTE KONTROLÜNDE EGZERSİZİN ROLÜ

Ayşegül ATLI [1]


Prader willi sendromu (PWS); beslenme bozuklukları, osteoporoz, fiziksel inaktivite, hipotoni, obezite, mental retardasyon, skolyoz ve gelişimsel gerilikler ile bireyi olumsuz etkileyen genetik bir bozukluktur Sendrom ilk olarak 1956'da Dr. Prader, Labhart ve Willi tarafından tanımlanmıştır. Paternal olarak türetilen kromozom 15'in uzun kolunda 11-13 segmentinin olmamasından kaynaklanır. Birbirini tetikleyen hipotoni, fiziksel inaktivite ve obezite için uygun egzersiz reçetelerine yönelik çalışmalar yapılmaktadır. Bebeklik döneminde zayıf emme beslenme eksikliğine neden olurken ilerleyen dönemlerde aşırı yeme davranışı obezite neden olur. Her iki durumda da bireyin gelişimine olumsuz etki eder. PWS’ye bağlı obezitenin tipik özelliği normal obez olan bireylere göre gövde ve bacaklarda daha fazla yağ kütlesi artışı olmasıdır. Cinsiyet farklılığına bakıldığında erkek bireylerde kadınlardan daha fazla yağ kütlesi artışına neden olur. Yiyecek isteme davranışı, istifleme yapmak veya yiyecek aramak, yiyecek almak için yiyecek veya para çalmak yaygındır. Hipotoni ve obezite arasında bağlantı vardır. Azalmış fiziksel aktivite ve yeme davranışındaki artma obeziteye zemin hazırlar. Hem Aerobik hem de anaerobik aktiviteler ile enerji tüketimini artırarak kilo kaybını sağlamak ve korumak için çok önemlidir. PWS’li bireyde ince ve kaba motor becerilerin geliştirilmesi, solunum kapasitesinin artırılması, osteoporozun önlenmesi orta ve hafif şiddetdeki egzersizler ile sağlanabilir. Hem bireysel eğitimin hem de grup içi egzersizlerin sosyal yönden bireyin gelişime etkisi büyüktür. Bu çalışmanın amacı genetik bir bozukluk olan PWS‘li bireylerin gelişimde obezite için egzersizin önemini vurgulamaktır.
PWS, egzersiz, obezite
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Orcid: 0000-0003-4879-1553
Yazar: Ayşegül ATLI (Sorumlu Yazar)
Kurum: ANKARA ÜNİVERSİTESİ
Ülke: Turkey


Destekleyen Kurum destekleyen kurum yoktur
Tarihler

Başvuru Tarihi : 30 Eylül 2020
Kabul Tarihi : 18 Mart 2021
Yayımlanma Tarihi : 30 Nisan 2021

APA Atlı, A . (2021). PRADER WİLLİ SENDROMU OLAN BİREYLERDE OBEZİTE KONTROLÜNDE EGZERSİZİN ROLÜ . International Anatolia Academic Online Journal Health Sciences , 7 (1) , 16-29 . Retrieved from https://dergipark.org.tr/tr/pub/iaaojh/issue/57725/802154