Agressive angiomyxoma: Case report

Abstract

Aggressive angiomyxoma is a rare benign mesenchymal neoplasm. It is often diagnosed in genital, pelvic and perineal region of women in reproductive ages. Aggressive angiomyxoma is associated with a high risk of local recurrence. Aggressive angiomyxoma is mixed with Bartholin\'s gland cyst, lipoma and vaginal cysts in diagnosis. Generally, stromal invasion is detected in these benign neoplasms. Therefore, wide local excision should be performed to treat. GnRH agonists could be administered in patient with aggressive angiomyxoma, either primary or recurrent. We reported a case with vulvar aggressive angiomyxoma presented with vulvar mass and treated with wide local excision.

Keywords

• Angiomyxoma, myxoma, vulvar mass

Agressive angiomyxoma: Case report

Öz

Agresif anjiomiksoma nadir görülen benign mezenşimal tümördür. Sıklıkla üreme çağı kadınlarda genital, pelvik ve perineal bölgelerde görülür. Agresif anjiomiksomada lokal rekürrens riski yüksektir. Tanıda agresif anjiomiksoma bartolin kisti, lipoma ve vajinal kist ile karışır. Bu iyi huylu tümörde genellikle stromal invazyon görülür ve geniş lokal eksizyon yapılmalıdır. GnRH agonistleri ile tedavi primer yada rekürren agresif anjiomiksoma olgularında uygulanabilir. Vulvar kitle tanısı ile geniş lokal eksizyon tedavisi uyguladığımız olguyu sunduk.

Anahtar Kelimeler

• Anjiomiksoma, miksoma, vulvar kitle

Kaynakça

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