Down Sendromu Anal Atrezi Pectus Carinatum ve Konjenital Hipotiroidinin Eşlik Ettiği Ventriküler Septal Defekt ve Konjenital Morgagni Hernisinin Sternotomi ile Başarılı Onarımı

Öz

Olgu sunumumuzda, 5 aylık Down sendromlu kız hastada yapılan başarılı konjenital Morgagni hernisi ve ventrikül septal defekt onarımını sunmaktayız. Median sternotomi yaklaşımıyla aynı seansta yapılan onarımlarda kardiyopulmoner bypass eşliğinde VSD, polytetrafluoroethylene yama ile kapatıldı. Diaframdaki defekt ise primer olarak, transabdominal yaklaşıma gerek olmadan onarıldı. Postoperatif seyir sorunsuzdu.

Anahtar Kelimeler

• Morgagni Hernisi
• Hipotiroidi
• Ventriküler Septal Defekt
• Anal Atrezi
• Pectus Carinatum

Successful Repair of Congenital Morgagni Hernia and Ventricular Septal Defect via Median Sternotomy in a Patient with Down Syndrome, Anal Atresia, Pectus Carinatum and Congenital Hypothyroidism

Öz

Here we report a 5-month-old female patient with Down syndrome who was successfully operated on due to congenital Morgagni hernia and ventricular septal defect concomitantly via median sternotomy. Ventricular septal defect was repaired with a polytetrafluoroethylene patch through the right atriotomy using cardiopulmonary bypass, and diaphragmatic hernia was repaired primarily with prolene sutures reinforced with teflon pledgets after excising the diaphragmatic hernia pouch simultaneously. Entire operation was completed via median sternotomy, and transabdominal approach was not required to repair the diaphragmatic hernia. Postoperative course was uneventful.

Anahtar Kelimeler

• Congenital Morgagni Hernia
• Ventricular Septal Defect
• Median Sternotomy
• Down Syndrome
• Anal Atresia
• Pectus Carinatum

Destekleyen Kurum

none

Kaynakça

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