Periyodik Ateş, Aftöz Stomatit, Farenjit ve Adenit PFAPA Sendromu: Dört Vakanın Sunumu

Öz

Periyodik ateş, aftöz stomatit, farenjit, adenit PFAPA sendromu, periyodik yüksek ateş dönemleri, aftöz stomatit, farenjit, ve servikal adenit ile karakterize, etiyolojisi bilin- meyen bir hastalıktır. Ender olarak görülmekle birlikte, sıklığının bildirilenden fazla olduğu düşünülmektedir. Bu makalede altı ay-bir yıldır üst solunum yolu enfeksiyonu semptomlarının eşlik ettiği yineleyen ateş atakları nedeni ile defalarca antibiyotik tedavisi alan ancak yalnızca oral kortikosteroid tedavisine dramatik yanıt veren PFAPA sendromlu dört çocuk hasta sunuldu. Yineleyen ateş, anti- biyotik ve antipiretiklere dirençli tonsillit ile başvuran çocuklarda PFAPA sendromu düşünülmelidir

Anahtar Kelimeler

• Çocukluk,periyodik ateş,PFAPA sendromu

Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis Syndrome: Report of Four Cases

Öz

PFAPA is a syndrome with unknown etiology which is cha- racterized by periodic fever episodes, aphthous stomatitis, pharyngitis and cervical adenitis. Although it is rare, its incidence is thought to be higher than it is reported. In this paper four children with PFAPA syndrome who have recei- ved antibiotherapies many times but responded only oral corticosteroid therapies dramatically were presented beca- use of recurring fever attacks accompanied by upper respi- ratory tract infection for six months-one year. PFAPA syndrome should be considered in children who presented with recurrent fever in addition to antibiotic and antipyre- tic- resistant tonsillitis

Anahtar Kelimeler

• Childhood,periodic fever,PFAPA syndrome

Kaynakça

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