Akut Lenfoblastik Löseminin Ender İlk Başvuru Bulgusu: Bilateral Nefromegali

Yıl 2017, Cilt: 17 Sayı: 1, 36 - 38, 01.01.2017

Enes Çelik Nurdan Yıldız Serçin Güven Emel Şenay İbrahim Gökçe

https://doi.org/10.5222/j.child.2017.036

https://izlik.org/JA46EU35KT

Öz

Akut lenfoblastik lösemi ALL çocukluk çağının en sık görülen kanseridir. Hastaların %8-16’sında klinik bulgu vermeyen böbrek tutulumu görülebilir, bunların çoğunda hasta lösemi tanısı aldıktan sonra böbrek tutulumu sapta- nır. Bu makalede karında şişkinlik nedeniyle başvuran, bilateral nefromegalisi olan ve tetkiklerin sonucunda pre B hücreli ALL tanısı alan 18 aylık vaka sunularak nefromega- linin ayırıcı tanısında lösemik infiltrasyonun önemi vurgu- landı

Anahtar Kelimeler

Nefromegali , akut lenfoblastik lösemi , böbrek tutulumu , lösemik infiltrasyon

An Unusual Cause of Bilateral Nephromegaly as the Rarely Seen First Presenting Finding of Acute Lymphoblastic Leukemia

https://izlik.org/JA46EU35KT

Öz

Acute lymphoblastic leukemia ALL is the most common type of cancer in childhood. Renal involvement may occur in 8-16% of patients without clinical manifestation and is detected in the majority of these cases renal involvement is detected after the patient received diagnosis of leukemia.. In this article, we presented a 18 month-old girl presented with abdominal distension and bilateral nephromegaly who was diagnosed with pre-B cell B-cell precursor acute lymphob- lastic leukemia, and emphasized that lymphoblastic infiltra- tion should be considered in the differential diagnosis of a patient presenting with unexplained nephromegaly

Anahtar Kelimeler

Nephromegaly , acute lymphoblastic leukemia , renal involvement , lymphoblastic infiltration

Kaynakça

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