Akut Lenfoblastik Löseminin Ender İlk Başvuru Bulgusu: Bilateral Nefromegali

Yıl 2017, , 36 - 38, 01.01.2017

Enes Çelik Nurdan Yıldız Serçin Güven Emel Şenay İbrahim Gökçe

https://doi.org/10.5222/j.child.2017.036

Öz

Akut lenfoblastik lösemi ALL çocukluk çağının en sık görülen kanseridir. Hastaların %8-16’sında klinik bulgu vermeyen böbrek tutulumu görülebilir, bunların çoğunda hasta lösemi tanısı aldıktan sonra böbrek tutulumu sapta- nır. Bu makalede karında şişkinlik nedeniyle başvuran, bilateral nefromegalisi olan ve tetkiklerin sonucunda pre B hücreli ALL tanısı alan 18 aylık vaka sunularak nefromega- linin ayırıcı tanısında lösemik infiltrasyonun önemi vurgu- landı

Anahtar Kelimeler

Nefromegali, akut lenfoblastik lösemi, böbrek tutulumu, lösemik infiltrasyon

An Unusual Cause of Bilateral Nephromegaly as the Rarely Seen First Presenting Finding of Acute Lymphoblastic Leukemia

Öz

Acute lymphoblastic leukemia ALL is the most common type of cancer in childhood. Renal involvement may occur in 8-16% of patients without clinical manifestation and is detected in the majority of these cases renal involvement is detected after the patient received diagnosis of leukemia.. In this article, we presented a 18 month-old girl presented with abdominal distension and bilateral nephromegaly who was diagnosed with pre-B cell B-cell precursor acute lymphob- lastic leukemia, and emphasized that lymphoblastic infiltra- tion should be considered in the differential diagnosis of a patient presenting with unexplained nephromegaly

Anahtar Kelimeler

Nephromegaly, acute lymphoblastic leukemia, renal involvement, lymphoblastic infiltration

Kaynakça

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