Konjenital Böbrek Anomalileri

Öz

Konjenital organ malformasyonları arasında en sık görü- len anomali böbrek ve üreterin konjenital anomalileridir. Üriner sistem enfeksiyonu, hipertansiyon ve böbrek yeter- sizliğine yol açması nedeni ile önemli morbiditeye sahip hastalıklardır. Çocuklarda son dönem böbrek yetersizliği nedenlerinin %30-50’sini oluşturur. Genetik olarak hetero- jen hastalıklardır, fakat tek gen hastalıkları veya kromozom bozuklukları da anomaliye yol açabilir. Bu anomaliler alt ya da üst üriner sistem anomalileri olarak görülebilir. Bu yazıda böbreğin üst üriner sistem konjenital malformas- yonları değerlendirilmiştir

Anahtar Kelimeler

• Konjenital,böbrek,çocuk,anomali,renal

Congenital Malformations of Kidney

Öz

The most common congenital organ anomalies in human beings are congenital anomalies of the kidney and the uri- nary tract CAKUT , which as a whole is an important cause of morbidity due to such complications as urinary tract infections, hypertension, and renal failure. Up to 30-50% of the end- stage renal disease is due to CAKUT. CAKUT is a group of genetically heterogeneous, but single gene disor- ders or chromosomal abnormalities which can lead to these anomalies. These anomalies can involve both the lower and/ or upper urinary tract. Congenital malformations of the kidney upper urinary tract were evaluated in this paper

Anahtar Kelimeler

• Congenital,kidney,renal,malformation,child

Kaynakça

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