Konjenital Kistik Adenomatoid Malformasyon: Bir Vaka Sunumu

Yıl 2012, , 193 - 197, 01.10.2012

Şenol Bozdağ Şirin Güven Çiğdem Yanar Ayanoğlu Hülya Yavuz Müferret Ergüven

https://doi.org/10.5222/j.child.2012.193

Öz

Konjenital kistik adenomatoid malformasyon, hamartama- töz veya displastik akciğer dokusunun, immatür bronş ağacından anormal dallanmasıyla oluşan, ender görülen konjenital bir pulmoner anomalidir. Bu lezyonların çoğu- nun tanısı prenatal ultrasonografi ile konulur. Yenidoğan döneminde en sık akut solunum sıkıntısı semptomları ile ortaya çıkar ve anormal akciğer grafi bulgusu veya bilgi- sayarlı toraks tomografisi ile doğrulanır. Burada prenatal tanısı olmayan ve yaşamın ilk günlerinde solunum sıkıntısı semptomları ile kliniğimize başvuran bu vaka sunularak, ender görülen konjenital kistik adenomatoid malformasyo- nun tartışılması amaçlandı

Anahtar Kelimeler

Konjenital kistik adenomatoid malformasyon, prenatal ultrasonografi, yenidoğan

Congenital Cystic Adenomatoid Malformation: A Case Report

Öz

Congenital cystic adenomatoid malformation, is a rare congenital pulmonary anomaly, which arises from imma- ture abnormal bronchial tree to form hamartomatous or dysplastic lung tissue. Most of these lesions were diagno- sed by prenatal ultrasound. The most common symptoms in the neonatal period is characterized by acute respiratory distress and confirmed by abnormal chest radiograph or computed thorax tomography. Here we aimed to discuss a rare case with congenital cystic adenomatoid malformati- on, presenting with symptoms of respiratory distress in the first days of life with no prenatal diagnosis

Anahtar Kelimeler

Congenital cystic adenomatoid malformation, newborn, prenatal ultrasound

Kaynakça

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