Wolf Parkinson White Sendromuna Sekonder Gelişen Bir Non İmmün Hidrops Vakası

Öz

Hidrops fetalis, en az iki fetal boşlukta sıvı toplanması veya ödem ile karakterize nonspesifik bir klinik tablodur. Geçmişte hidropsun en sık nedeni Rh alloimmünizasyona bağlı eritroblastozis fetalis iken, günümüzde hidrops vakalarının çoğunu non-immün hidrops oluşturmaktadır. Non-immün hidrops fetalis insidansı 1:830-1:4600/ canlı doğum arasındadır. Non-immün hidropsa sıklıkla kromo- zomal bozukluklar, kardiyak malformasyonlar, aritmiler, TORCH grubu infeksiyonlar ve talasemiler eşlik eder. Tıp alanındaki gelişmelere rağmen, non-immün hidrops feta- lisin mortalitesi halen yüksektir. Bu makalede hidrops ve fetal distres nedeniyle 28. gebelik haftasında sezaryen ile doğan, hipoalbüminemi ve masif proteinüri nedeniyle nefrotik sendrom ön tanısı düşünülen, ancak izlemde Wolf Parkinson White Sendromu tanısı alan bir non-immün hidrops vakası literatür bilgileri ışığında sunuldu

Anahtar Kelimeler

• Non-immün,hidrops fetalis,Wolf Parkinson White sendromu

A Case of Non-Immune Hydrops Fetalis Caused by Wolf-Parkinson-White Syndrome

Öz

Hydrops fetalis is a nonspecific clinical condition characte- rized by an accumulation of fluid in at least two fetal com- partments or edema. In the past, most of the cases of hydrops were caused by erythroblastosis fetalis related to Rh alloim- munisation, while today most of them were induced by non- immune conditions. The incidence of non-immune hydrops fetalis is 1:830-4600 per live births. Non-immune hydrops fetalis is mostly associated with chromosomal disorders, cardiac malformations, arrhythmias, and TORCH infecti- ons. Despite advances in medicine, the mortality of non- immune hydrops fetalis is still high. In this report, an infant with non-immune hydrops fetalis born at 28th week of gesta- tional age by caeseran section due to hydrops and fetal distress and previously considered to be congenital nephro- tic syndrome because of hypoalbuminemia and massive proteinuria, but diagnosed to be Wolf-Parkinson-White Syndrome is presented with literature highlights

Anahtar Kelimeler

• Non-immune,hydrops fetalis,Wolf-ParkinsonWhite syndrome

Kaynakça

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