Konjenital Kistik Adenomatoid Malformasyon: Bir Vaka Sunumu

Yıl 2012, Cilt: 12 Sayı: 4, 193 - 197, 01.10.2012

Şenol Bozdağ Şirin Güven Çiğdem Yanar Ayanoğlu Hülya Yavuz Müferret Ergüven

https://doi.org/10.5222/j.child.2012.193

Öz

Konjenital kistik adenomatoid malformasyon, hamartama- töz veya displastik akciğer dokusunun, immatür bronş ağacından anormal dallanmasıyla oluşan, ender görülen konjenital bir pulmoner anomalidir. Bu lezyonların çoğu- nun tanısı prenatal ultrasonografi ile konulur. Yenidoğan döneminde en sık akut solunum sıkıntısı semptomları ile ortaya çıkar ve anormal akciğer grafi bulgusu veya bilgi- sayarlı toraks tomografisi ile doğrulanır. Burada prenatal tanısı olmayan ve yaşamın ilk günlerinde solunum sıkıntısı semptomları ile kliniğimize başvuran bu vaka sunularak, ender görülen konjenital kistik adenomatoid malformasyo- nun tartışılması amaçlandı

Anahtar Kelimeler

Konjenital kistik adenomatoid malformasyon, prenatal ultrasonografi, yenidoğan

Congenital Cystic Adenomatoid Malformation: A Case Report

Öz

Congenital cystic adenomatoid malformation, is a rare congenital pulmonary anomaly, which arises from imma- ture abnormal bronchial tree to form hamartomatous or dysplastic lung tissue. Most of these lesions were diagno- sed by prenatal ultrasound. The most common symptoms in the neonatal period is characterized by acute respiratory distress and confirmed by abnormal chest radiograph or computed thorax tomography. Here we aimed to discuss a rare case with congenital cystic adenomatoid malformati- on, presenting with symptoms of respiratory distress in the first days of life with no prenatal diagnosis

Anahtar Kelimeler

Congenital cystic adenomatoid malformation, newborn, prenatal ultrasound

Kaynakça

• van dijk C, Wagenvoort Ca. The various types of congeni- tal adenomatoid malformation of the lung. J Pathol ;110:131-4. http://dx.doi.org/10.1002/path.1711100204 PMid:4125873 ting the lung parenchyma. In contemporary diagnosis and management of neonatal respiratory diseases. Newton, PA
• Handbooks in Health Care Co; 1995: 164-179. of one lung with general anasarca. Arch Pathol 1949;48:221
• Salles M, deschildre a, Bonnel C, et al. Diagnostic et traite- ment des malformations bronchopulmonaires congénitales: analyse de 32 observations. Arch Pediatr 2005;12:1703-8. http://dx.doi.org/10.1016/j.arcped.2005.09.013 PMid:16226879
• Neonatal outcome of antenatally diagnosed congenital cystic adenomatoid malformations. Ultrasound Obstet Gynecol ;26:150-3. http://dx.doi.org/10.1002/uog.1920 PMid:16038013 malformation of the lung: A report of 17 cases and review of the literature. Pathol Annu 1980;158:387-402.
• Congenital cystic adenomatoid malformation in an adult pre- senting as lung abscess. Eur J Cardiothorac Surg 2000;18:720- http://dx.doi.org/10.1016/S1010-7940(00)00578-9 mation in the newborn: two case studies and review of the literature. Respiratory Care 2000;45(10):1188-95. PMid:11054898
• (eds). Pediatric Pathology 2nd ed. Philadelphia: Lippincott/ Williams & Wilkins, 2001: 445-517. malformation of the lung. A report of 17 cases and review of the literature. Pathol Ann 1980;15:382-402.
• Is there a difference between the antenatally and postnatally diagnosed cases? Pediatr Radiol 2005;35:79-84. http://dx.doi.org/10.1007/s00247-004-1331-4 PMid:15480617 matoid malformation of the lung: Review of genetics, prenatal diagnosis, and in utero treatment. Am J Med Genet A ;140:151-5. http://dx.doi.org/10.1002/ajmg.a.31031 PMid:16353256
• Congenital cystic adenomatoid malformation in an adult pre- senting as lung abscess. Eur J Cardio-Thorac Surg ;18:720-3. http://dx.doi.org/10.1016/S1010-7940(00)00578-9
• Franken Ea Jr, Buehl I. Bebekile lobar emphysema. Report of two cases with unusual roentgenographic manifestation. Am J Roentgenol Radium Ther Nucl Med 1966: 354-357. PMid:5925106
• Howell lJ. Fetal lung lesions: management and outcome. American Journal of Obstetrics and Gynecology 1998;179: 9. http://dx.doi.org/10.1016/S0002-9378(98)70183-8