Hemophagocytic Syndrome; A Mortal Progressing Case Despite Early Diagnosis and Treatment

Öz

In this case we discussed with a hemaphagocytic syndrome in a patient who was investigated for jaundice. Hemophagocytic syndrome; fever, hypertriglyceridemia, hepatosplenomegaly, bone marrow involvement is a multisystemic disease.This is due to excess cytokines released from the cells.Hemophagocytic syndrome, can occur as a familial or sporadic disorder, and it can be triggered by a variety of events that disrupt immune homeostasis.

Anahtar Kelimeler

• Hemophagocytic syndrome
• jaundice
• pancytopenia

Hemofagositik sendrom, erken tanıya rağmen mortal seyreden bir olgu

Öz

In this case we discussed with a hemaphagocytic syndrome in a patient who was investigated for jaundice. Hemophagocytic syndrome; fever, hypertriglyceridemia, hepatosplenomegaly, bone marrow involvement is a multisystemic disease.This is due to excess cytokines released from the cells.Hemophagocytic syndrome, can occur as a familial or sporadic disorder, and it can be triggered by a variety of events that disrupt immune homeostasis.

Anahtar Kelimeler

• hemafagositik sendrom
• ikter
• pansitopeni

Kaynakça

1. Rederans1 How I treat hemophagocytic lymphohistiocytosis. Jordan MB, Allen CE, Weitzman S, Filipovich AH, McClain KL, Blood. 2011;118(15):4041. Epub 2011 Aug 9. Referans2 The unique aspects of presentation and diagnosis of hemophagocytic lymphohistiocytosis in adults.Nikiforow S, Berliner N. Hematology Am Soc Hematol Educ Program. 2015;2015:183-9.