Fahr Hastalığı ve Hipoparatiroidi ile Olan İlişkisi: Olgu Sunumu

Öz

Fahr hastalığı çeşitli ilerleyici nöro-psikolojik ve bilişsel belirtilerle seyreden ve kranial BT’de simetrik bazal gangliyon kalsifikasyonu ile karakterize bir hastalıktır. Fahr hastalığı’nın hipoksi, radyasyon, sistemik hastalıklar, toksinler, paratiroid hormon ve kalsiyum metabolizması ve ensefalitler ile bağlantılı olduğu ileri sürülmüştür. Bu yazıda hipoparatiroidi ile ilişkili Fahr hastalığı tanısı konan 34 yaşındaki kadın hasta sunuldu.

Anahtar Kelimeler

• Fahr hastalığı, Bazal Ganglion kalsifikasyonu, hipoparatroidizm

Fahr’s Disease and Its Relationship with Hypoparathyroidism: Case Report

Öz

Fahr’s disease is characterized by a variety of progressive neuropsychological and cognitive symptoms and symmetric basal ganglia calcifications on cranial CT. The related conditions which may cause Fahr’s disease are hypoxia, radiation, systemic disorders, toxins, disorders of the parathyroid hormones, aberrant calcium metabolism and encephalitis. In this article, we present a 34-year-old female patient diagnosed with Fahr’s disease associated with hypoparathyroidism

Anahtar Kelimeler

• Fahr’s disease, Basal Ganglia calcification, hypoparathyroidism

Kaynakça

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