Sodyum Kanal Blokeri ile Ortaya Çıkarılan Brugada Sendromu

Öz

Giriş: Brugada sendromu yapısal olarak normal kalpte sağ prekordiyal elektrokardiyografi (EKG) leadlerde ST segment elevasyonu ve artmış ani kardiyak ölüm riski ile karakterizedir. Klinik olarak atipik göğüs ağrısı, çarpıntı, senkop, supraventriküler taşikardi,ventriküler taşikardi, ventriküler fibrilasyon, ani ölüm şeklinde karşılaşılabilir. Olgu Sunumu: Otuz dokuz yaşında erkek hasta çarpıntı, presenkop şikayeti ile kliniğimize başvurdu. Presenkop, ailede ani ölüm öyküsü ve EKG bulguları bir arada değerlendirilen hastada ön tanı olarak brugada sendromu düşünüldü. Tanıyı doğrulamak için hastaya ajmanil verilerek provakasyon testi uygulandı. Seri çekilen EKG’lerini değerlendirildi ve hastada Brugada sendromu tanısını doğrulayan Tip 1 EKG örneği gözlendi. Sonuç: Amacımız Brugada sendromu düşünülen vakalarda tanı koymaya yardımcı bir yöntem olan sodyum kanal blokerlerinin kullanımını, vaka üzerinden tartışmak ve tanı kolaylığı sağlayacak yöntemi tanıtmaktır.

Anahtar Kelimeler

• Brugada sendromu, ani kardiyak ölüm, ajmaline

Brugada Syndrome was Uncovered with a Sodium Channel Blocker

Öz

Introduction: The Brugada syndrome is characterized by an STsegment elevation in the right precordial electrocardiography (ECG) leads and a high incidence of sudden death in patients with structurally normal hearts. Clinically, atypical chest pain, palpitations, syncope, supraventricular tachycardia, ventricular tachycardia, ventricular fibrillation and sudden death may occur. Case Report: A 39 year old male patient was admitted with presyncope and palpitation symptoms to our clinic. A family history of sudden death presyncope and ECG findings brought the Brugada syndrome as a differential diagnosis to mind. To confirm the diagnosis, a provacation test with ajmanil was done. Serial performed ECGs have been evaluated and a Type 1 ECG sample which confirms the Brugada Syndrome has been observed in the patient.Conclusion: Our goal is to help make the diagnosis of Brugada syndrome cases, a method comprising the use of the sodium channel blockers, and discuss case studies to introduce the method to provide ease of diagnosis

Anahtar Kelimeler

• Brugada syndrome, sudden cardiac death, ajmaline

Kaynakça

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