Wunderlich's syndrome as the fatal complication of a renal angiomyolipoma: a case report and review of the literature

Yıl 2019, Cilt: 2 Sayı: 4, 153 - 155, 22.09.2019

Fatma Zeynep Arslan , Ayşegül Altunkeser

https://doi.org/10.32322/jhsm.496356

Öz

Wunderlich
syndrome (WS) is a rare acute abdominal condition, which is  characterized with spontaneous nontraumatic
renal haemorrhage into the subcapsular and perirenal spaces. Renal cell
carcinoma, angiomyolipoma, renal cysts, vasculitis or blood dyscrasias are
among the known risk factors. We
report a case of Wunderlich's syndrome in an 59 year old woman associated with
massive retroperitoneal hemorrhage.

Anahtar Kelimeler

Wunderlich syndrome, angiomyolipoma, computed tomography

Renal anjiyomiyolipomun ölümcül komplikasyonu olarak Wunderlich sendromu: olgu sunumu ve literatürün gözden geçirilmesi

Öz

Wunderlich sendromu (WS), subkapsüler ve perirenal boşluklara nonumumatik renal kanama ile ilişkili nadir bir akut karın hastalığıdır. Renal hücreli karsinom, anjiyomiyolipom, böbrek kistleri, vaskülit veya kan disprasileri bilinen risk faktörleri arasındadır. Masif retroperitoneal kanama ile ilişkili 59 yaşındaki bir kadın hastada Wunderlich sendromu olgusunu sunuyoruz.

Anahtar Kelimeler

Wunderlich sendromu, anjiyomiyolipom, bilgisayarlı tomografi

Kaynakça

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• 3. Ramon J., Rimon U., Garniek A. “ZARenal angiomyolipoma: long-term results following selective arterial embolization,” European Urology, vol. 55, no. 5, pp. 1155–1162, 2009
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